POEMS syndrome

POEMS syndrome is a paraneoplastic syndrome characterized by polyradiculoneuropathy (P), organomegaly (O), endocrinopathy (E), clonal plasma cell disorder (M), and skin changes (S). Other features include papilledema, extravascular volume overload, sclerotic bone lesions, thrombocytosis/erythrocytosis, and elevated VEGF levels.

Portal hypertension

Increased pressure in the portal vein.


Total: 11

                      


(per page)
PMID (PMCID)
28247771
FEMALE Middle Aged
POEMS syndrome and idiopathic portal hypertension: a possible association.
Campos S, Agostinho C, Cipriano MA.
Rev Esp Enferm Dig. 2017;109(5):393.
POEMS syndrome and idiopathic portal hypertension: a possible association.
28503308
(5425989)
OTHER
Portal hypertension as the initial manifestation of POEMS syndrome: a case report.
Wu L, Li Y, Yao F, Lu C, Li J, Zhou W, Qian J.
BMC Hematol. 2017;17:9.
Lenalidomide with or without dexamethasone is effective for portal hypertension due to POEMS syndrome, though esophageal and gastric varices seems not reversible so easily.
28503308
(5425989)
OTHER
Portal hypertension as the initial manifestation of POEMS syndrome: a case report.
Wu L, Li Y, Yao F, Lu C, Li J, Zhou W, Qian J.
BMC Hematol. 2017;17:9.
This case highlights the manifestation of portal hypertension in POEMS syndrome.
28503308
(5425989)
OTHER
Portal hypertension as the initial manifestation of POEMS syndrome: a case report.
Wu L, Li Y, Yao F, Lu C, Li J, Zhou W, Qian J.
BMC Hematol. 2017;17:9.
In differential diagnosis of portal hypertension, POEMS syndrome should be considered especially when other symptoms such as numbness, organomegaly, endocrine alteration and skin changes also present, as it is highlighted by our case.
20403034
FEMALE Adult
POEMS syndrome with idiopathic portal hypertension: autopsy case and review of the literature.
Inoue R, Nakazawa A, Tsukada N, Katoh Y, Nagao T, Nakanuma Y, Mukai K.
Pathol Int. 2010;60(4):316-20.
Portal hypertension is a rare symptom in POEMS syndrome.
20403034
FEMALE Adult
POEMS syndrome with idiopathic portal hypertension: autopsy case and review of the literature.
Inoue R, Nakazawa A, Tsukada N, Katoh Y, Nagao T, Nakanuma Y, Mukai K.
Pathol Int. 2010;60(4):316-20.
Reported herein is an autopsy case of POEMS syndrome in a subject who developed idiopathic portal hypertension (IPH).
20403034
FEMALE Adult
POEMS syndrome with idiopathic portal hypertension: autopsy case and review of the literature.
Inoue R, Nakazawa A, Tsukada N, Katoh Y, Nagao T, Nakanuma Y, Mukai K.
Pathol Int. 2010;60(4):316-20.
POEMS syndrome with idiopathic portal hypertension: autopsy case and review of the literature.
10978936
FEMALE Middle Aged
Reversible pulmonary hypertension in POEMS syndrome--another etiology of triggered pulmonary vasculopathy?
Paciocco G, Bossone E, Erba H, Rubenfire M.
Can J Cardiol. 2000;16(8):1007-12.
POEMS syndrome, like anorexigens, cocaine, portal hypertension and human immunodeficiency virus infection, may be another trigger for the pulmonary vascular occlusive process found in primary pulmonary hypertension.
10051986
MALE Middle Aged
[Portal hypertension and neutrocytic ascites in POEMS syndrome].
Stepani P, Courouble Y, Postel P, Mezieres P, Tossou H, Couvelard A, Trophilme D, Barbare JC, Bories C.
Gastroenterol Clin Biol. 1998;22(12):1095-7.
[Portal hypertension and neutrocytic ascites in POEMS syndrome].
10051986
MALE Middle Aged
[Portal hypertension and neutrocytic ascites in POEMS syndrome].
Stepani P, Courouble Y, Postel P, Mezieres P, Tossou H, Couvelard A, Trophilme D, Barbare JC, Bories C.
Gastroenterol Clin Biol. 1998;22(12):1095-7.
Portal hypertension is rare in POEMS syndrome and this is the first time that culture negative neutrocytic ascites has been described with this syndrome.
10051986
MALE Middle Aged
[Portal hypertension and neutrocytic ascites in POEMS syndrome].
Stepani P, Courouble Y, Postel P, Mezieres P, Tossou H, Couvelard A, Trophilme D, Barbare JC, Bories C.
Gastroenterol Clin Biol. 1998;22(12):1095-7.
We report a case of portal hypertension and neutrocytic ascites in a 52 year old man with POEMS syndrome.