POEMS syndrome

POEMS syndrome is a paraneoplastic syndrome characterized by polyradiculoneuropathy (P), organomegaly (O), endocrinopathy (E), clonal plasma cell disorder (M), and skin changes (S). Other features include papilledema, extravascular volume overload, sclerotic bone lesions, thrombocytosis/erythrocytosis, and elevated VEGF levels.

Immunodeficiency

Failure of the immune system to protect the body adequately from infection, due to the absence or insufficiency of some component process or substance.


合計: 2

                      


(表示件数)
PMID (PMCID)
21326077
FEMALE Adult
Concomitant Castleman's disease and sarcoidosis.
Rice BL, Farver CF, Pohlman B, Burkey BB, Parambil JG.
Am J Med Sci. 2011;341(3):257-9.
This disorder has frequently been associated with several systemic syndromes, including human immunodeficiency virus infection, polyneuropathy, organomegaly, endocrinopathy, monoclonal gammopathy and skin changes (POEMS) syndrome and various connective tissue diseases.
10978936
FEMALE Middle Aged
Reversible pulmonary hypertension in POEMS syndrome--another etiology of triggered pulmonary vasculopathy?
Paciocco G, Bossone E, Erba H, Rubenfire M.
Can J Cardiol. 2000;16(8):1007-12.
POEMS syndrome, like anorexigens, cocaine, portal hypertension and human immunodeficiency virus infection, may be another trigger for the pulmonary vascular occlusive process found in primary pulmonary hypertension.