POEMS syndrome

POEMS syndrome is a paraneoplastic syndrome characterized by polyradiculoneuropathy (P), organomegaly (O), endocrinopathy (E), clonal plasma cell disorder (M), and skin changes (S). Other features include papilledema, extravascular volume overload, sclerotic bone lesions, thrombocytosis/erythrocytosis, and elevated VEGF levels.

Lymphoproliferative disorder



Total: 4

                       


(per page)
PMID (PMCID)
30310290
(6166759)
 OTHER
POEMS syndrome complicated with multiple ischemic vascular events: case report and review of literature.
Gaman M, Vladareanu AM, Dobrea C, Onisai M, Marinescu C, Cisleanu D, Ciufu C, Vasile D, Bumbea H, Voican I.
Onco Targets Ther. 2018;11:6271-6276.
Castleman disease (CD) is a rare lymphoproliferative disorder, closely related to POEMS syndrome; ~11%-30% of POEMS patients are associated with concomitant CD.
26722578
 MALE Young Adult
Castleman disease variant of POEMS syndrome complicated with multiple cerebral infarction: a rare case report and review of literature.
Yu H, Yao F, Li Y, Li J, Cui QC.
Int J Clin Exp Pathol. 2015;8(10):13578-83.
Castleman disease is a lymphoproliferative disorder that can be present in POEMS patients, which can be defined as Castleman disease variant of POEMS syndrome.
18035247
 MIXED_SAMPLE Middle Aged
Recurrent strokes in two patients with POEMS syndrome and Castleman's disease.
Garcia T, Dafer R, Hocker S, Schneck M, Barton K, Biller J.
J Stroke Cerebrovasc Dis. 2007;16(6):278-84.
Castleman's disease is a rare lymphoproliferative disorder that can be present in patients with POEMS syndrome.
15678710
 FEMALE Middle Aged
Calciphylaxis in a patient with POEMS syndrome without renal failure and/or hyperparathyroidism. A case report.
De Roma I, Filotico R, Cea M, Procaccio P, Perosa F.
Ann Ital Med Int. 2004;19(4):283-7.
POEMS (Crow-Fukase) syndrome is a rare plasma cell lymphoproliferative disorder associated with polyneuropathy (P), organomegaly (O), endocrinopathy (E), monoclonal (M) gammopathy and skin (S) abnormalities.