Constriction rings syndrome

Constriction rings syndrome is a congenital limb malformation disorder with an extremely variable clinical presentation characterized by the presence of partial to complete, congenital, fibrous, circumferential, constriction bands/rings on any part of the body, although a particular predilection for the upper or lower extremities is seen. Phenotypes range from only a mild skin indentation to complete amputation of parts of the fetus (e.g. digits, distal limb). Compression from the rings may lead to edema, skeletal anomalies (e.g. fractures, foot deformities) and, infrequently, neural compromise.

Gangrene

A serious and potentially life-threatening condition that arises when a considerable mass of body tissue dies (necrosis).

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PMID (PMCID)
14996111	FEMALE	Infant, Newborn
	Congenital Volkmann ischaemic contracture: a case report and review.
	Cham PM, Drolet BA, Segura AD, Esterly NB. Br J Dermatol. 2004;150(2):357-63.
	Because the lesions can be mistaken for other entities including necrotizing fasciitis, neonatal gangrene, congenital varicella, aplasia cutis congenita, amniotic band syndrome, subcutaneous fat necrosis and epidermolysis bullosa, dermatologists play a significant role in the diagnosis and, consequently, the treatment of the patient.
7683901	MIXED_SAMPLE	Infant, Newborn
	[Congenital paralysis due to compression. Apropos of 4 cases].
	Rombouts JJ, Debauche C, Verellen G, Lyon G. Ann Chir Main Memb Super. 1993;12(1):39-44.
	Congenital dysfunction of major peripheral nerves have been described as a complication of congenital constriction band syndrome, in association with subcutaneous fat necrosis, neonatal gangrene or aplasia cutis congenita.