Congenital pulmonary valve stenosis

Congenital pulmonary stenosis (PS) is a congenital heart malformation (see this term) that is characterized by a right ventricular outflow obstruction with a clinical presentation that may vary from critical stenosis presenting in the neonatal period to asymptomatic mild stenosis. The obstruction in PS can be at the valvular, subpulmonary, or supravalvular levels (valvular, subpulmonary, supravalvular PS; see these terms).

Cirrhosis

A chronic disorder of the liver in which liver tissue becomes scarred and is partially replaced by regenerative nodules and fibrotic tissue resulting in loss of liver function.


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(per page)
PMID (PMCID)
29364100
FEMALE Middle Aged
Unsuccessful transjugular intrahepatic portosystemic shunt for a patient with right heart failure and portal hypertension.
Graus L, Verresen L, De Vusser P, Verbrugge FH, Caenepeel P.
Acta Gastroenterol Belg. 2017;80(1):63-66.
A 60-year-old women with a history of congenital pulmonary valve stenosis developed right heart failure, cardiac cirrhosis and end-stage renal disease requiring renal replacement therapy.