Autoimmune lymphoproliferative syndrome

A rare, inherited disorder characterized by non-malignant lymphoproliferation, multilineage cytopenias, and a lifelong increased risk of Hodgkin's and non-Hodgkin's lymphoma.

Arthritis

Inflammation of a joint.


Total: 1

                      


(per page)
PMID (PMCID)
25669891
MALE Infant
Association of severe myoclonic epilepsy of infancy (SMEI) with probable autoimmune lymphoproliferative syndrome-variant.
Berio A, Mangiante G, Piazzi A.
Pediatr Med Chir. 2014;36(5-6):100.
The diagnosis of probable autoimmune lymphoproliferative syndrome was made; arthritis, skin and throat blisters, which appeared subsequently led to the diagnosis of linear IgA disease.