Truncus arteriosus

Truncus arteriosus (TA) is a rare congenital cardiovascular anomaly characterized by a single arterial trunk arising from the heart by means of a single semilunar valve (<I>i.e.</I> truncal valve). Pulmonary arteries originate from the common arterial trunk distal to the coronary arteries and proximal to the first brachiocephalic branch of the aortic arch. TA typically overrides a large outlet ventricular septal defect (VSD). The intracardiac anatomy usually displays situs solitus and atrioventricular (AV) concordance.

Pulmonary artery stenosis

An abnormal narrowing or constriction of the pulmonary artery, in the main pulmonary artery and/or in the left or right pulmonary artery branches.


Total: 8

                      


(per page)
PMID (PMCID)
29034225
(5626947)
OTHER
The Perception of a Three-Dimensional-Printed Heart Model from the Perspective of Different Stakeholders: A Complex Case of Truncus Arteriosus.
Biglino G, Moharem-Elgamal S, Lee M, Tulloh R, Caputo M.
Front Pediatr. 2017;5:209.
The patient has a right aortic arch, a repaired truncus arteriosus, pulmonary artery stenosis, as well as conduit stenosis, with a complex surgical plan being discussed.
20082465
MIXED_SAMPLE
Pancreatic hypoplasia presenting with neonatal diabetes mellitus in association with congenital heart defect and developmental delay.
Balasubramanian M, Shield JP, Acerini CL, Walker J, Ellard S, Marchand M, Polak M, Vaxillaire M, Crolla JA, Bunyan DJ, Mackay DJ, Temple IK.
Am J Med Genet A. 2010;152A(2):340-6.
In addition, Patient 1 had a ventricular septal defect, patent ductus arteriosus and pulmonary artery stenosis; Patient 2 had a truncus arteriosus and Patient 3 had tetralogy of Fallot.
17311774
MIXED_SAMPLE Infant
Demonstration of coronary arteries and major cardiac vascular structures in congenital heart disease by cardiac multidetector computed tomography angiography.
Dogan OF, Karcaaltincaba M, Yorgancioglu C, Demircin M, Dogan R, Ersoy U, Celiker A, Alehan D, Haliloglu M, Boke E.
Heart Surg Forum. 2007;10(1):E90-4.
Pulmonary vascular bed findings were also confirmed during surgery in patients with TF and in one patient with truncus arteriosus type I and severe left pulmonary artery stenosis.
17311774
MIXED_SAMPLE Infant
Demonstration of coronary arteries and major cardiac vascular structures in congenital heart disease by cardiac multidetector computed tomography angiography.
Dogan OF, Karcaaltincaba M, Yorgancioglu C, Demircin M, Dogan R, Ersoy U, Celiker A, Alehan D, Haliloglu M, Boke E.
Heart Surg Forum. 2007;10(1):E90-4.
The other 3 patients had truncus arteriosus and severe left pulmonary artery stenosis (n = 1), double outlet right ventricle (n = 1), and Kawasaki disease (n = 1) with suspected coronary artery aneurysms.
9402663
FEMALE Infant, Newborn
Open heart interventions in premature low- and very-low-birth-weight neonates: risk profile and ethical considerations.
Borowski A, Schickendantz S, Mennicken U, Korb H.
Thorac Cardiovasc Surg. 1997;45(5):238-41.
Two premature neonates with low and very low birth weight of 1160 g and 1650 g, were operated on using cardiopulmonary bypass for severe pulmonary artery stenosis and truncus arteriosus communis type II, respectively.
9316541
MIXED_SAMPLE Infant
Truncus arteriosus communis associated with chromosome 22q11 deletion.
Momma K, Ando M, Matsuoka R.
J Am Coll Cardiol. 1997;30(4):1067-71.
In truncus arteriosus communis, the rare type A3 with major aortopulmonary collateral arteries and pulmonary ostial stenosis and type A1 with pulmonary artery stenosis are associated with del 22q11.
9316541
MIXED_SAMPLE Infant
Truncus arteriosus communis associated with chromosome 22q11 deletion.
Momma K, Ando M, Matsuoka R.
J Am Coll Cardiol. 1997;30(4):1067-71.
The other three had type A1 truncus arteriosus and pulmonary artery stenosis.
8561570
OTHER Infant
Early pulmonary homograft failure from dilatation due to distal pulmonary artery stenosis.
DeLeon SY, Tuchek JM, Bell TJ, Hofstra J, Vitullo DA, Quinones JA, Fisher EA.
Ann Thorac Surg. 1996;61(1):234-6; discussion 236-7.
Early progressive pulmonary homograft insufficiency developed in an 11-month-old infant after repair of truncus arteriosus because of dilatation secondary to the presence of residual distal pulmonary artery stenosis and hypoplasia.