Goldenhar syndrome

Goldenhar syndrome (GS), also known as oculo-auriculo-vertebral dysplasia (OAV), is a rare developmental syndrome characterized by a classic triad of mandibular hypoplasia resulting in facial asymmetry, ear and/or eye malformations, and vertebral anomalies.

Dermoid cyst

A congenital subcutaneous cyst that arises from entrapment of skin along the lines of embryonic fusion. In contrast to epidermal cysts, dermoid cysts tend to contain various adnexal structures such as hair, sebaceous, eccrine or apocrine glands. Dermoid cysts are present at birth, and are indolent, firm, deep, subcutaneous nodules. They are often located on the head and neck, and rarely in the anogenital area. Dermoid cysts are\nslowly progressive and can grow to a size of 1 to 4 cm.

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PMID (PMCID)
21305808	FEMALE	Adult
	Goldenhar syndrome: ocular features.
	Bhallil S, Benatiya I, El Abdouni O, Mahjoubi B, Hicham T. Bull Soc Belge Ophtalmol. 2010;(316):17-9.
	Goldenhar syndrome is a rare congenital anomaly which consists of a triad of an ocular dermoid cyst, preauricular skin tags and vertebral dysplasia.
17992045	MALE	Child
	Posterior fossa dermoid cyst in a patient with Goldenhar syndrome.
	Dange N, Bonde V, Goel A, Muzumdar D. Pediatr Neurosurg. 2007;43(6):522-5.
	A 7-year-old boy with Goldenhar syndrome was diagnosed to have a posterior cranial fossa dermoid cyst.