Goldenhar syndrome

Goldenhar syndrome (GS), also known as oculo-auriculo-vertebral dysplasia (OAV), is a rare developmental syndrome characterized by a classic triad of mandibular hypoplasia resulting in facial asymmetry, ear and/or eye malformations, and vertebral anomalies.

Polyotia

The presence of an extra auricle on one or both sides of the head.


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PMID (PMCID)
16877912
 FEMALE Infant
Goldenhar complex with atypical associated anomalies: is the spectrum still widening?
Konas E, Canter HI, Mavili ME.
J Craniofac Surg. 2006;17(4):669-72.
Here we report a patient presenting goldenhar syndrome with accessory auricula, defined as polyotia, coloboma and bifid tongue.