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Langerhans cell histiocytosis

Langerhans cell histiocytosis (LCH) is a systemic disease associated with the proliferation and accumulation (usually in granulomas) of Langerhans cells in various tissues.

Xanthelasma

The presence of xanthomata in the skin of the eyelid.

Total: 1

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PMID (PMCID)
28128149	OTHER
	Multifocal Langerhans Cell Granulomatosis (Hand-schuller - Christian Disease).
	Sawhney M, Shakatwat RS, Roy BM, Khetarpal A, Verma SK. Indian J Dermatol Venereol Leprol. 1989;55(5):329-330.
	A 47 year old female developed multifocal Langerhans cell granulomatosis (Hand-Schuller-Christian disease) manifesting as papulo-pustular, nodular, crusted and scaly lesions, xanthelasma, ulceration of gingival mucosa with loss of teeth, vaginal granulomatosis, diabetes insipidus, multiple osteolytic bone lesions and honeycombing of the lungs.