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Langerhans cell histiocytosis

Langerhans cell histiocytosis (LCH) is a systemic disease associated with the proliferation and accumulation (usually in granulomas) of Langerhans cells in various tissues.

Cerebellar atrophy

Atrophy (wasting) of the cerebellum.

Total: 1

(per page)

PMID (PMCID)
15864184	MALE
	[Langerhans cell histiocytosis in an adult patient associated with sclerosing cholangitis and cerebellar atrophy].
	Desrame J, Bechade D, Defuentes G, Goasdoue P, Raynaud JJ, Claude V, Renard JL, Genereau T, Coutant G, Algayres JP. Gastroenterol Clin Biol. 2005;29(3):300-3.
	We report a case of Langerhans' cell histiocytosis in an adult with sclerosing cholangitis which rapidly progressed to fatal liver failure and progressive cerebellar atrophy.