Langerhans cell histiocytosis

Langerhans cell histiocytosis (LCH) is a systemic disease associated with the proliferation and accumulation (usually in granulomas) of Langerhans cells in various tissues.

Pulmonary infiltrates



合計: 2

                      


(表示件数)
PMID (PMCID)
28360976
(5355761)
OTHER
Langerhans cell histiocytosis masquerading as acute appendicitis: Case report and review.
Karimzada MM, Matthews MN, French SW, DeUgarte D, Kim DY.
World J Gastrointest Endosc. 2017;9(3):139-144.
Langerhans cell histiocytosis (LCH) is a rare syndrome characterized by unifocal, multifocal unisystem, or disseminated/multi-system disease that commonly involves the bone, skin, lymph nodes, pituitary, or sometimes lung (almost exclusively in smokers) causing a variety of symptoms from rashes and bone lesions to diabetes insipidus or pulmonary infiltrates.
8061649
FEMALE Adult
[Recurrent infections of the respiratory tract and staphylococcal pneumonia with septic shock and total respiratory failure in a patient with histiocytosis X].
Wawrzynska L, Meleniewska-Maciszewska A, Burakowski J.
Pneumonol Alergol Pol. 1994;62(3-4):194-8.
Disseminated pulmonary infiltrates, cutaneous lesions and diabetes insipidus in a female patients with a history of recurrent pneumothorax and persistent respiratory tract infections suggested the diagnosis of histiocytosis X.