Langerhans cell histiocytosis

Langerhans cell histiocytosis (LCH) is a systemic disease associated with the proliferation and accumulation (usually in granulomas) of Langerhans cells in various tissues.

Biliary cirrhosis

Progressive destruction of the small-to-medium bile ducts of the intrahepatic biliary tree, which leads to progressive cholestasis and often end-stage liver disease.


Total: 2

                       


(per page)
PMID (PMCID)
15022067
 MIXED_SAMPLE Infant
Liver involvement in the histiocytic disorders of childhood.
Jaffe R.
Pediatr Dev Pathol. 2004;7(3):214-25.
Early involvement is by Langerhans cell histiocytosis (LCH) infiltration leading to a sclerosing cholangitis and, eventually, biliary cirrhosis.
12025455
 FEMALE Middle Aged
[Secondary biliary cirrhosis in a patient with histiocytosis X].
Romao Z, Pontes J, Andrade P, Leitao MC, Donato A, Freitas D.
Acta Med Port. 2002;15(1):55-9.
[Secondary biliary cirrhosis in a patient with histiocytosis X].