Langerhans cell histiocytosis

Langerhans cell histiocytosis (LCH) is a systemic disease associated with the proliferation and accumulation (usually in granulomas) of Langerhans cells in various tissues.

Granulomatosis

A granulomatous inflammation leading to multiple granuloma formation, which is a specific type of inflammation. A granuloma is a focal compact collection of inflammatory cells, mononuclear cells predominating, usually as a result of the persistence of a non-degradable product and of active cell mediated hypersensitivity.


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PMID (PMCID)
19886712
 MIXED_SAMPLE
Common diagnostic challenges in the pathology of nonneoplastic lung diseases: a case-based review.
Lagstein A, Myers JL.
Arch Pathol Lab Med. 2009;133(11):1782-92.
Our goal is that readers gain a greater understanding of those features most helpful in recognizing usual interstitial pneumonia, Langerhans cell histiocytosis, aspiration pneumonia, and Wegener granulomatosis.
12148090
 MALE Middle Aged
Psychoneuroendocrine disturbances in a patient with a rare granulomatous disease.
Perras B, Petersen D, Lorch H, Fehm HL.
Exp Clin Endocrinol Diabetes. 2002;110(5):248-52.
Erdheim-Chester disease (ECD) and Langerhans' cell histiocytosis (LCH) are rare granulomatosis-like diseases of unknown etiology which are characterized by lipoidgranulomatous infiltrates in various organs.
8159358
 FEMALE Adult
Pregnancy in a patient with eosinophilic granulomatosis of the lung: a case report.
Mitra AG, Turpin SV, Cefalo RC.
Obstet Gynecol. 1994;83(5 Pt 2):811-3.
There are three syndromes of histiocytosis X: eosinophilic granulomatosis of the lungs, Hand-Schuller-Christian disease, and Letterer-Siwe disease.
28128149
 OTHER
Multifocal Langerhans Cell Granulomatosis (Hand-schuller - Christian Disease).
Sawhney M, Shakatwat RS, Roy BM, Khetarpal A, Verma SK.
Indian J Dermatol Venereol Leprol. 1989;55(5):329-330.
A 47 year old female developed multifocal Langerhans cell granulomatosis (Hand-Schuller-Christian disease) manifesting as papulo-pustular, nodular, crusted and scaly lesions, xanthelasma, ulceration of gingival mucosa with loss of teeth, vaginal granulomatosis, diabetes insipidus, multiple osteolytic bone lesions and honeycombing of the lungs.
300532
 MALE Adult
[Histiocytosis X (eosinophilic granulomatosis) of the lung (author's transl)].
Stanulla H.
Zentralbl Allg Pathol. 1977;121(1-2):108-13.
[Histiocytosis X (eosinophilic granulomatosis) of the lung (author's transl)].
1081314
 MALE Adult
[Unusual generalized granulomatosis. Two case reports (author's transl)].
Schafer RJ, Feichter GE.
Zentralbl Allg Pathol. 1975;119(1-2):104-10.
The unusual cerebral features in the second case - diagnosed as disseminated eosinophilic granulomatosis - seem to show some relations to histiocytosis X.