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Langerhans cell histiocytosis

Langerhans cell histiocytosis (LCH) is a systemic disease associated with the proliferation and accumulation (usually in granulomas) of Langerhans cells in various tissues.

Paraproteinemia

An abnormal immunoglobulin or part of an Ig (light chain) in the circulation. Paraproteins are typically produced by a clonal population of B-cell derived plasma cells.

Total: 1

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PMID (PMCID)
19354333	MALE	Young Adult
	Cutaneous normolipemic plane xanthoma with supraglottic involvement in a patient with hand-Schuller-Christian Disease: a case report.
	Lu YT, Chen TJ, Chung WH, Kuo TT, Hong HS. Am J Clin Dermatol. 2009;10(3):189-92.
	Association with systemic disease or paraproteinemia has been reported previously, but rarely with Langerhans cell histiocytosis (LCH).