Williams-Campbell syndrome


Respiratory failure

A severe form of respiratory insufficiency characterized by inadequate gas exchange such that the levels of oxygen or carbon dioxide cannot be maintained within normal limits.


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PMID (PMCID)
22348466
(4066632)
 MALE Adult
Lung transplantation for Williams-Campbell syndrome with a probable familial association.
Burguete SR, Levine SM, Restrepo MI, Angel LF, Levine DJ, Coalson JJ, Peters JI.
Respir Care. 2012;57(9):1505-8.
Williams-Campbell syndrome is a rare disorder characterized by deficiency of subsegmental bronchial cartilage and development of airway collapse and bronchiectasis that may subsequently progress to respiratory failure and death.
21841334
 MALE Adult
Respiratory failure of Williams-Campbell syndrome is effectively treated by noninvasive positive pressure ventilation.
Wada H, Seto R, Yamada H, Nagao T, Hajiro T, Nakano Y.
Intern Med. 2011;50(16):1729-32.
Williams-Campbell syndrome is a rare disease, characterized by a congenital deficiency of cartilage in the fourth to sixth order bronchi, leading to chronic respiratory failure with recurrent pulmonary infections.
21841334
 MALE Adult
Respiratory failure of Williams-Campbell syndrome is effectively treated by noninvasive positive pressure ventilation.
Wada H, Seto R, Yamada H, Nagao T, Hajiro T, Nakano Y.
Intern Med. 2011;50(16):1729-32.
NPPV may have an advantage in adults with Williams-Campbell syndrome who have severe respiratory failure and recurrent pulmonary infections.
16423213
 FEMALE
CT bronchoscopy in the diagnosis of Williams-Campbell syndrome.
George J, Jain R, Tariq SM.
Respirology. 2006;11(1):117-9.
The authors report a patient with Williams-Campbell syndrome with type II respiratory failure due to extensive cystic bronchiectasis and secondary emphysema.
10410549
 MALE
[Severe adult-type Williams-Campbell syndrome (Williams-Campbell-type bronchiectasis)].
Kimoto T, Kawamura T, Nakahara Y, Mochizuki Y.
Nihon Kokyuki Gakkai Zasshi. 1999;37(5):429-32.
Compared with previous cases of Williams-Campbell syndrome reported in Japan, this case was interesting because the patient exhibited severe respiratory failure and because the dilatating and collapsing bronchi were demonstrated by fluoroscopy.