IgG4-related kidney disease

A rare renal disease occurring in the setting of a systemic IgG4 related disease. Renal manifestations include tubulointerstitial nephritis (TIN), membranous glomerulonephritis with or without TIN, IgA nephropathy, membranoproliferative glomerulonephritis, mesangioproliferative immune complex glomerulonephritis, sclerosing pyelitis, IgG4-related plasma cell arteritis, and hydronephrosis associated with IgG4 related retroperitoneal fibrosis or ureteral inflammatory pseudotumor. Patients present with acute or chronic renal failure and radiographic mass lesion.

Glomerulonephritis

Inflammation of the renal glomeruli.


Total: 2

                       


(per page)
PMID (PMCID)
27504450
(4965529)
 OTHER
Coexistence of Acute Crescent Glomerulonephritis and IgG4-Related Kidney Disease.
Lu Z, Yin J, Bao H, Jiao Q, Wu H, Wu R, Xue Q, Wang N, Zhang Z, Wang F.
Case Rep Nephrol Dial. 2016;6(2):89-95.
Coexistence of Acute Crescent Glomerulonephritis and IgG4-Related Kidney Disease.
26502965
(4624354)
 FEMALE
Membranoproliferative glomerulonephritis with predominant IgG2 and IgG3 deposition in a patient with IgG4-related disease.
Ueki K, Matsukuma Y, Masutani K, Tsuchimoto A, Fujisaki K, Torisu K, Tanaka S, Kiyoshima T, Hisano S, Kitazono T, Tsuruya K.
BMC Nephrol. 2015;16:173.
The favorable clinical course in our patient suggests that steroid therapy is promising in cases of IgG4-related kidney disease accompanied by glomerulonephritis.