IgG4-related kidney disease

A rare renal disease occurring in the setting of a systemic IgG4 related disease. Renal manifestations include tubulointerstitial nephritis (TIN), membranous glomerulonephritis with or without TIN, IgA nephropathy, membranoproliferative glomerulonephritis, mesangioproliferative immune complex glomerulonephritis, sclerosing pyelitis, IgG4-related plasma cell arteritis, and hydronephrosis associated with IgG4 related retroperitoneal fibrosis or ureteral inflammatory pseudotumor. Patients present with acute or chronic renal failure and radiographic mass lesion.

Membranous nephropathy

A type of glomerulonephropathy characterized by thickening of the basement membrane and deposition of immune complexes in the subepithelial space.

Total: 2

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PMID (PMCID)
29709946 (6207830)	MALE	Middle Aged
	A Refractory Case of Secondary Membranous Nephropathy Concurrent with IgG4-related Tubulointerstitial Nephritis.
	Arai H, Toda N, Kamimatsuse R, Nishioka K, Endo S, Akiyama S, Maruyama S, Matsubara T, Yokoi H, Yanagita M. Intern Med. 2018;57(19):2873-2877.
	Membranous nephropathy is a rare manifestation of IgG4-related kidney disease.
25849674 (4360725)	OTHER
	Acute Interstitial Nephritis and Membranous Nephropathy in the Context of IgG4-Related Disease.
	Stylianou K, Maragkaki E, Tzanakakis M, Stratakis S, Gakiopoulou H, Daphnis E. Case Rep Nephrol Dial. 2015;5(1):44-8.
	The biopsy revealed IgG4-related kidney disease with severe interstitial nephritis and membranous nephropathy.