Incontinentia pigmenti

Incontinentia pigmenti (IP) is a rare X-linked dominant multi-systemic ectodermal dysplasia usually lethal in males and presenting neonatally in females with a bullous rash along Blashko's lines (BL) followed by verrucous plaques evolving over time to hyperpigmented swirling patterns. It is further characterized by teeth abnormalities, alopecia, nail dystrophy and affects occasionally the retina and the central nervous system (CNS).

Hemiparesis

Loss of strength in the arm, leg, and sometimes face on one side of the body. Hemiplegia refers to a complete loss of strength, whereas hemiparesis refers to an incomplete loss of strength.

Total: 2

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PMID (PMCID)
8198677	FEMALE
	Vascular occlusion associated with incontinentia pigmenti.
	Pellegrino RJ, Shah AJ. Pediatr Neurol. 1994;10(1):73-4.
	A 4 1/2-year-old girl with incontinentia pigmenti developed acute-onset hemiparesis.
2043371	FEMALE	Child
	[Cerebral white matter lesions in a case of incontinentia pigmenti with infantile spasms, mental retardation and left hemiparesis].
	Sasaki M, Hanaoka S, Suzuki H, Takashima S, Arima M. No To Hattatsu. 1991;23(3):278-83.
	[Cerebral white matter lesions in a case of incontinentia pigmenti with infantile spasms, mental retardation and left hemiparesis].