Incontinentia pigmenti

Incontinentia pigmenti (IP) is a rare X-linked dominant multi-systemic ectodermal dysplasia usually lethal in males and presenting neonatally in females with a bullous rash along Blashko's lines (BL) followed by verrucous plaques evolving over time to hyperpigmented swirling patterns. It is further characterized by teeth abnormalities, alopecia, nail dystrophy and affects occasionally the retina and the central nervous system (CNS).

Meningitis

Inflammation of the meninges.

Total: 1

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PMID (PMCID)
3902309	FEMALE	Child
	Actinomycosis meningitis in a girl with incontinentia pigmenti.
	Diamantopoulos N, Bergman I, Kaplan S. Clin Pediatr (Phila). 1985;24(11):651-4.
	A 7-year-old girl with incontinentia pigmenti and a history of multiple bacterial infections developed chronic meningitis with Actinomycosis odontolyticus, which was successfully treated with long-term penicillin administration.