Incontinentia pigmenti

Incontinentia pigmenti (IP) is a rare X-linked dominant multi-systemic ectodermal dysplasia usually lethal in males and presenting neonatally in females with a bullous rash along Blashko's lines (BL) followed by verrucous plaques evolving over time to hyperpigmented swirling patterns. It is further characterized by teeth abnormalities, alopecia, nail dystrophy and affects occasionally the retina and the central nervous system (CNS).

Leukemia

A cancer of the blood and bone marrow characterized by an abnormal proliferation of leukocytes.

Total: 2

(per page)

PMID (PMCID)
1059263	FEMALE	Infant
	Incontinentia pigmenti (Bloch-Sulzberger syndrome) associated with acute granulocytic leukemia.
	Rivera R, Cangir A, Strong L. South Med J. 1975;68(11):1391-4.
	Incontinentia pigmenti (Bloch-Sulzberger syndrome) associated with acute granulocytic leukemia.
1059263	FEMALE	Infant
	Incontinentia pigmenti (Bloch-Sulzberger syndrome) associated with acute granulocytic leukemia.
	Rivera R, Cangir A, Strong L. South Med J. 1975;68(11):1391-4.
	Incontinentia pigmenti, a syndrome of developmental defects, was found to be associated with acute granulocytic leukemia in a 4-month-old black girl.