Incontinentia pigmenti

Incontinentia pigmenti (IP) is a rare X-linked dominant multi-systemic ectodermal dysplasia usually lethal in males and presenting neonatally in females with a bullous rash along Blashko's lines (BL) followed by verrucous plaques evolving over time to hyperpigmented swirling patterns. It is further characterized by teeth abnormalities, alopecia, nail dystrophy and affects occasionally the retina and the central nervous system (CNS).

Linear hyperpigmentation

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PMID (PMCID)
23613254	MIXED_SAMPLE
	X-linked reticulate pigmentary disorder with systemic manifestations: a new family and review of the literature.
	Pezzani L, Brena M, Callea M, Colombi M, Tadini G. Am J Med Genet A. 2013;161A(6):1414-20.
	In the carrier females, manifestations are apparently limited to the skin with patchy linear hyperpigmentation following the lines of Blaschko that are similar to stage III incontinentia pigmenti.