Incontinentia pigmenti

Incontinentia pigmenti (IP) is a rare X-linked dominant multi-systemic ectodermal dysplasia usually lethal in males and presenting neonatally in females with a bullous rash along Blashko's lines (BL) followed by verrucous plaques evolving over time to hyperpigmented swirling patterns. It is further characterized by teeth abnormalities, alopecia, nail dystrophy and affects occasionally the retina and the central nervous system (CNS).

Nail dystrophy

Onychodystrophy (nail dystrophy) refers to nail changes apart from changes of the color (nail dyschromia) and involves partial or complete disruption of the various keratinous layers of the nail plate.

Total: 3

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PMID (PMCID)
14674911	FEMALE	Middle Aged
	Nail dystrophy, an unusual presentation of incontinentia pigmenti.
	Nicolaou N, Graham-Brown RA. Br J Dermatol. 2003;149(6):1286-8.
	Nail dystrophy, an unusual presentation of incontinentia pigmenti.
12581087	FEMALE	Child
	Twenty-nail dystrophy in a girl with incontinentia pigmenti.
	Scardamaglia L, Howard A, Sinclair R. Australas J Dermatol. 2003;44(1):71-3.
	Twenty-nail dystrophy in a girl with incontinentia pigmenti.
12581087	FEMALE	Child
	Twenty-nail dystrophy in a girl with incontinentia pigmenti.
	Scardamaglia L, Howard A, Sinclair R. Australas J Dermatol. 2003;44(1):71-3.
	A 9-year-old girl with incontinentia pigmenti (IP) diagnosed soon after birth subsequently developed 20-nail dystrophy at the age of 3 years.