Incontinentia pigmenti

Incontinentia pigmenti (IP) is a rare X-linked dominant multi-systemic ectodermal dysplasia usually lethal in males and presenting neonatally in females with a bullous rash along Blashko's lines (BL) followed by verrucous plaques evolving over time to hyperpigmented swirling patterns. It is further characterized by teeth abnormalities, alopecia, nail dystrophy and affects occasionally the retina and the central nervous system (CNS).

Bacteremia

Presence of viable bacteria in the blood.

Total: 1

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PMID (PMCID)
677916	FEMALE	Infant
	Incontinentia pigmenti. Evidence for both neutrophil and lymphocyte dysfunction.
	Jessen RT, Van Epps DE, Goodwin JS, Bowerman J. Arch Dermatol. 1978;114(8):1182-6.
	A child with incontinentia pigmenti (Bloch-Sultzberger syndrome) had recurrent pneumococcal meningitis and pneumococcal bacteremia with associated subdural hematomas.