IgG4-related retroperitoneal fibrosis

Retroperitoneal fibrosis (RPF) is characterized by the development of a fibrotic mass surrounding retroperitoneal structures, such as aorta, vena cava, ureters and psoas muscle.

Splenomegaly

Abnormal increased size of the spleen.


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PMID (PMCID)
18365137
 MALE Adult
An unexpected cause of a febrile patient with huge splenomegaly.
Nonami A, Yamamoto H, Nakamura M, Nagafuji K, Teshima T.
Clin Rheumatol. 2008;27(7):941-3.
The differential diagnosis of huge splenomegaly with fever usually includes hematolymphoid malignancies and infectious diseases; however, our case was diagnosed as idiopathic retroperitoneal fibrosis.