Alagille syndrome

A rare syndrome variably characterized by chronic cholestasis due to paucity of intrahepatic bile ducts, peripheral pulmonary artery stenosis, vertebrae segmentation anomalies, characteristic facies, posterior embryotoxon/anterior segment abnormalities, pigmentary retinopathy, and dysplastic kidneys.

Pleural effusion

The presence of an excessive amount of fluid in the pleural cavity.


合計: 1

                       


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PMID (PMCID)
12234275
 MALE Infant
Repeated detection of gas in the portal vein after liver transplantation: A sign of EBV-associated post-transplant lymphoproliferation?
Wallot MA, Klepper J, Clapuyt P, Dirsch O, Malago M, Reding R, Otte JB, Sokal EM.
Pediatr Transplant. 2002;6(4):332-6.
A 1-yr-old child presented with intractable right sided pleural effusion and progressive clinical deterioration 3 weeks after liver transplantation for Alagille Syndrome.