Alagille syndrome

A rare syndrome variably characterized by chronic cholestasis due to paucity of intrahepatic bile ducts, peripheral pulmonary artery stenosis, vertebrae segmentation anomalies, characteristic facies, posterior embryotoxon/anterior segment abnormalities, pigmentary retinopathy, and dysplastic kidneys.

Hyperlipidemia

An elevated lipid concentration in the blood.


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PMID (PMCID)
2101790
 MALE Child
Effects of various doses of growth hormone on serum total cholesterol, phospholipid, and bile acid in a patient with cholestasis.
Noda H, Sato H, Nakajima H.
Endocrinol Jpn. 1990;37(6):851-5.
To determine whether growth hormone (GH) has any impact on the hyperlipidemia seen in cholestatic patients, graded doses of GH in the sequence of 0.1, 0.2, 0.4, and 0.6 u/kg every other day were administered sc to a patient with Alagille syndrome.