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Alagille syndrome

A rare syndrome variably characterized by chronic cholestasis due to paucity of intrahepatic bile ducts, peripheral pulmonary artery stenosis, vertebrae segmentation anomalies, characteristic facies, posterior embryotoxon/anterior segment abnormalities, pigmentary retinopathy, and dysplastic kidneys.

Malnutrition

Total: 1

(per page)

PMID (PMCID)
10400102	MIXED_SAMPLE	Infant
	Percutaneous endoscopic gastrostomy for continuous feeding in children with chronic cholestasis.
	Duche M, Habes D, Lababidi A, Chardot C, Wenz J, Bernard O. J Pediatr Gastroenterol Nutr. 1999;29(1):42-5.
	Percutaneous endoscopic gastrostomy was performed in five children (age range, 20 months to 13 years) with severe cholestasis (Alagille syndrome in four; biliary atresia in one) and severe malnutrition (mean weight, -2.6 standard deviations; mean height, -2.7 standard deviations) who were awaiting liver transplantation.