Left ventricular noncompaction

Left ventricular noncompaction (LVNC) is a rare cardiomyopathy characterized anatomically by prominent left ventricular trabeculae and deep intratrabecular recesses causing progressive systolic and diastolic dysfunction, conduction abnormalities, and occasionally thromboembolic events.

Pierre-Robin sequence

Pierre Robin malformation is a sequence of developmental malformations characterized by micrognathia (mandibular hypoplasia), glossoptosis and cleft palate.


Total: 1

                      


(per page)
PMID (PMCID)
22447382
FEMALE Infant, Newborn
Isolated left ventricular noncompaction in a newborn with Pierre-Robin sequence.
Aypar E, Sert A, Gokmen Z, Aslan E, Odabas D.
Pediatr Cardiol. 2013;34(2):452-4.
Isolated left ventricular noncompaction in a newborn with Pierre-Robin sequence.