Cystic fibrosis

Cystic fibrosis (CF) is a genetic disorder characterized by the production of sweat with a high salt content and mucus secretions with an abnormal viscosity.

Hypertension

The presence of chronic increased pressure in the systemic arterial system.


Total: 17

                       


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PMID (PMCID)
26412053
 FEMALE Adult
Renin-associated hypertension after bronchial artery embolization in cystic fibrosis.
Coolen N, Gouya H, Kanaan R, Honore I, Chapron J, Hubert D, Legmann P, Dusser D, Burgel PR.
J Cyst Fibros. 2016;15(2):213-5.
Renin-associated hypertension after bronchial artery embolization in cystic fibrosis.
26855654
(4735539)
 OTHER
Single lung transplantation in a patient with retrospective positive cross-match.
Lesinska AJ, Piotrowska M, Dec P, Wasilewski P, Kubisa A, Pierog J, Wojcik N, Czarnecka M, Kubisa B, Grodzki T.
Kardiochir Torakochirurgia Pol. 2015;12(4):351-4.
Lung transplantation is a method useful in such non-malignant end-stage parenchymal and vascular diseases as: chronic obstructive pulmonary disease (COPD), idiopathic interstitial pulmonary fibrosis, cystic fibrosis, or primary pulmonary hypertension.
22624431
 MALE
Atypical presentation of cystic fibrosis--obese adolescent with hypertension and pseudo-Bartter's syndrome.
Sovtic A, Minic P, Bogdanovic R, Stajic N, Rodic M, Markovic-Sovtic G.
Vojnosanit Pregl. 2012;69(4):367-9.
To our knowledge, this is the first reported case of atypical presentation of cystic fibrosis in an adolescent presented with pseudo-Bartter's syndrome and signs of obesity and hypertension.
22624431
 MALE
Atypical presentation of cystic fibrosis--obese adolescent with hypertension and pseudo-Bartter's syndrome.
Sovtic A, Minic P, Bogdanovic R, Stajic N, Rodic M, Markovic-Sovtic G.
Vojnosanit Pregl. 2012;69(4):367-9.
Atypical presentation of cystic fibrosis--obese adolescent with hypertension and pseudo-Bartter's syndrome.
22266831
 FEMALE Infant, Newborn
Cystic fibrosis: an unusual neonatal presentation.
Sankaran K, Kalapurackal M, Wiebe S.
Pediatr Pulmonol. 2012;47(6):620-2.
In this report we describe a neonate born with cystic fibrosis (CF) who presented to us with hypoxic respiratory failure, pulmonary hypertension, and hypercarbia without lactic acedemia from sticky mucous plugging and massive lung collapse.
16479610
 MALE Adult
Effects of sildenafil on pulmonary hypertension and exercise tolerance in severe cystic fibrosis-related lung disease.
Montgomery GS, Sagel SD, Taylor AL, Abman SH.
Pediatr Pulmonol. 2006;41(4):383-5.
Cystic fibrosis (CF) patients with advanced lung disease are at risk for developing pulmonary vascular disease and pulmonary hypertension, characterized by progressive exercise intolerance beyond the exercise-limiting effects of airways disease in CF.
16479610
 MALE Adult
Effects of sildenafil on pulmonary hypertension and exercise tolerance in severe cystic fibrosis-related lung disease.
Montgomery GS, Sagel SD, Taylor AL, Abman SH.
Pediatr Pulmonol. 2006;41(4):383-5.
Effects of sildenafil on pulmonary hypertension and exercise tolerance in severe cystic fibrosis-related lung disease.
15337084
 FEMALE Adult
Aerosolized iloprost as a bridge to lung transplantation in a patient with cystic fibrosis and pulmonary hypertension.
Tissieres P, Nicod L, Barazzone-Argiroffo C, Rimensberger PC, Beghetti M.
Ann Thorac Surg. 2004;78(3):e48-50.
We describe a patient with cystic fibrosis, end-stage lung disease, and secondary pulmonary hypertension in whom aerosolized iloprost was effective in lowering pulmonary artery pressure and improving functional status, thus proving successful as a bridge to lung transplantation.
15337084
 FEMALE Adult
Aerosolized iloprost as a bridge to lung transplantation in a patient with cystic fibrosis and pulmonary hypertension.
Tissieres P, Nicod L, Barazzone-Argiroffo C, Rimensberger PC, Beghetti M.
Ann Thorac Surg. 2004;78(3):e48-50.
Aerosolized iloprost as a bridge to lung transplantation in a patient with cystic fibrosis and pulmonary hypertension.
12719971
 MALE
Rapidly developing Cushing syndrome in a 4-year-old patient during combined treatment with itraconazole and inhaled budesonide.
De Wachter E, Vanbesien J, De Schutter I, Malfroot A, De Schepper J.
Eur J Pediatr. 2003;162(7-8):488-489.
A 4-year-old boy with cystic fibrosis developed hypertension, rapid weight gain and a moon face 2 weeks after starting a combined treatment of oral itraconazole and inhaled budesonide for a suspected allergic bronchopulmonary aspergillosis.
12831974
 MALE Adult
[Posterior reversible encephalopathy syndrome: about 2 cases related to the cyclosporine].
Lepoivre T, Treilhaud M, Auffray-Calvier E, Rigal JC, Blanloeil Y.
Ann Fr Anesth Reanim. 2003;22(5):466-9.
Following a pulmonary transplantation for cystic fibrosis, 2 patients exhibited a syndrome associating arterial hypertension, headache, visual trouble and generalized seizures.
11975963
 FEMALE
Cystic fibrosis and hemolytic uremic syndrome coexisting during pregnancy.
Plante LA, Ortega E.
Obstet Gynecol. 2002;99(5 Pt 2):930-2.
An 18-year-old primigravida with cystic fibrosis was admitted at term with pulmonary symptoms, hypertension, and thrombocytopenia.
9588587
 MIXED_SAMPLE Adult
Pulmonary capillaritis: a possible histologic form of acute pulmonary allograft rejection.
Badesch DB, Zamora M, Fullerton D, Weill D, Tuder R, Grover F, Schwarz MI.
J Heart Lung Transplant. 1998;17(4):415-22.
We report five cases of pulmonary capillaritis with a histologic appearance distinct from typical rejection, occurring in patients ranging in age from 18 to 45 years, with a variety of underlying diseases including alpha1 antitrypsin deficiency, pulmonary hypertension, cystic fibrosis, and rheumatoid arthritis.
8098790
 MIXED_SAMPLE Adult
Aetiology of asthma: lessons from lung transplantation.
Corris PA, Dark JH.
Lancet. 1993;341(8857):1369-71.
We have done lung transplants in two such patients; and we have also transplanted the lungs from two mildly asthmatic patients, whose death was unrelated to their asthma, into two patients with end-stage cystic fibrosis and primary pulmonary hypertension, respectively.
7679172
 FEMALE Child
Pediatric lung transplantation. The years 1985 to 1992 and the clinical trial of FK 506.
Armitage JM, Fricker FJ, Kurland G, Hardesty RL, Michaels M, Morita S, Starzl TE, Yousem SA, Jaffe R, Griffith BP.
J Thorac Cardiovasc Surg. 1993;105(2):337-45; discussion 346.
The causes of end-stage lung disease were primary pulmonary hypertension (n = 7), congenital heart disease (n = 5), cystic fibrosis (n = 4), pulmonary arteriovenous malformation (n = 2), graft-versus-host disease (n = 1), and desquamative interstitial pneumonitis (n = 1).
1943955
 MIXED_SAMPLE Adult
The "domino-donor" operation in heart and lung transplantation.
Cochrane AD, Smith JA, Esmore DS.
Med J Aust. 1991;155(9):589-93.
The first domino-donor was a 25-year-old man with cystic fibrosis and pulmonary hypertension, receiving a heart-lung transplant, whose heart was transplanted into a 20-year-old woman with end-stage cardiomyopathy.
3688757
 FEMALE Adult
Vocal cord paralysis associated with cystic fibrosis.
Zitsch RP, Reilly JS.
Ann Otol Rhinol Laryngol. 1987;96(6):680-3.
Pulmonary artery hypertension and dilation occur in up to 80% of patients with cystic fibrosis.