Cystic fibrosis

Cystic fibrosis (CF) is a genetic disorder characterized by the production of sweat with a high salt content and mucus secretions with an abnormal viscosity.

Pneumonia

Inflammation of any part of the lung parenchyma.


Total: 38

                       


(per page)
PMID (PMCID)
30345929
 OTHER
Burkholderia cepacia Complex Causing Pneumonia in an Immunocompetent Non-Cystic Fibrosis Patient: Case Report and Review of Literature.
Datta P, Gupta M, Kumar MB, Gupta V, Chander J.
Infect Disord Drug Targets. 2018;:.
Burkholderia cepacia Complex Causing Pneumonia in an Immunocompetent Non-Cystic Fibrosis Patient: Case Report and Review of Literature.
27143075
 MIXED_SAMPLE Infant, Newborn
[Molecular diagnosis of two Chinese cystic fibrosis children and literature review].
Xu BP, Wang H, Zhao YH, Liu J, Yao Y, Feng XL, Shen KL.
Zhonghua Er Ke Za Zhi. 2016;54(5):344-8.
One of the two newly diagnosed cystic fibrosis cases was a 10-year old girl who suffered from reccurent cough with expectoration and associated with cirrhosis.Sweat tests showed increased chloride twice with the lower level of 306.82 mmol/L.The other was an 8-month old boy with reccurent pneumonia from neonate, failure to thrive and fatty diarrhea.Two children had various degrees of bronchiectasis and massive sticky secretion on the bronchoscopy.They had no family history and their parents had no consanguineous marriage.CFTR mutations of c. 595C>T and c. 2290C>T were found in gene tests.On the database, twenty-one reports involving thirty-six Chinese patients (16 males and 20 females) were retrieved.Together with this group of 2 cases, a total of 38 cases were involved.The age at diagnosis was 4 months to 28 years with a median age of 10 years.All patients had reccurent respiratory infections, twenty-seven cases (71%) had malnutrition, fifteen (39%)had chronic diarrhea, and 16 cases (42%) had other digestive manifestations, including jaundice (4 cases), hepatomegaly (11 cases), ascites (2 cases) and pancreatic atrophy (3 cases).
25562561
 FEMALE
A 15-year old girl with asthma and lower lobe bronchiectasis.
Ricketti PA, Unkle DW, King KA, Cleri DJ, Ricketti AJ.
Allergy Asthma Proc. 2015;36(1):82-6.
The differential diagnosis includes cystic fibrosis (CF), immunodeficiency disorders, complement deficiency, allergic bronchopulmonary aspergillosis, alpha-1 antitrypsin disease, repeated aspiration pneumonia, foreign body, bronchial carcinoid, unresolved right middle lobe pneumonia, and primary ciliary dyskinesia (PCD).
25299375
 FEMALE Young Adult
Lung transplant for a patient with cystic fibrosis and active Burkholderia Cenocepacia pneumonia.
Salizzoni S, Pilewski J, Toyoda Y.
Exp Clin Transplant. 2014;12(5):487-9.
Lung transplant for a patient with cystic fibrosis and active Burkholderia Cenocepacia pneumonia.
25299375
 FEMALE Young Adult
Lung transplant for a patient with cystic fibrosis and active Burkholderia Cenocepacia pneumonia.
Salizzoni S, Pilewski J, Toyoda Y.
Exp Clin Transplant. 2014;12(5):487-9.
This case suggests that patients who have cystic fibrosis and active B. Cenocepacia pneumonia may be successfully treated with a lung transplant.
25299375
 FEMALE Young Adult
Lung transplant for a patient with cystic fibrosis and active Burkholderia Cenocepacia pneumonia.
Salizzoni S, Pilewski J, Toyoda Y.
Exp Clin Transplant. 2014;12(5):487-9.
A 24-year-old white woman who had cystic fibrosis presented with respiratory failure caused by B. Cenocepacia pneumonia.
24832699
 MALE Young Adult
Panton-Valentine Leukocidin-positive Staphylococcus aureus: a potentially significant pathogen in cystic fibrosis.
Barry PJ, Isalska BJ, Jones AM.
Paediatr Respir Rev. 2014;15 Suppl 1:22-5.
We describe a further case of pneumonia in a patient with cystic fibrosis, and outline potential transmission of the organism from healthy family members to this patient.
24968502
 MALE Infant
Cystic fibrosis presenting with persistent pneumonia --a case study of a 3-month-old adopted baby.
Lodh M, Joshi AK.
J Indian Med Assoc. 2013;111(10):699, 703.
Cystic fibrosis presenting with persistent pneumonia --a case study of a 3-month-old adopted baby.
22684986
 MALE Infant
Invasive pneumonia and septic shock in infants as a presentation of cystic fibrosis with vitamin-deficiency.
Al-Khadra ES, Chau KW, Barone CP, Colin AA.
Pediatr Pulmonol. 2012;47(7):722-6.
Invasive pneumonia and septic shock in infants as a presentation of cystic fibrosis with vitamin-deficiency.
22292927
 FEMALE Adult
The role of post-transplantation cyclosporine treatment in the course of cystic fibrosis pulmonary disease: a case report.
Tesse R, Manca A, Abrusci MR, Pinto S, Leonetti G, De Robertis S, Cavallo L, De Robertis F.
Immunopharmacol Immunotoxicol. 2012;34(4):714-6.
We describe the case of a 44-year-old female cystic fibrosis (CF) patient (R334W/852del22) who presented symptoms of prolonged acute respiratory infections and recurrent episodes of pneumonia.
21752969
 FEMALE Adult
First case of Segniliparus rotundus pneumonia in a patient with bronchiectasis.
Koh WJ, Choi GE, Lee SH, Park YK, Lee NY, Shin SJ.
J Clin Microbiol. 2011;49(9):3403-5.
We report the first case of Segniliparus rotundus pneumonia in an adult with non-cystic fibrosis bronchiectasis.
21220216
 FEMALE Young Adult
KPC-2 carbapenemase-producing Klebsiella pneumoniae isolates from patients with Cystic Fibrosis.
Leao RS, Pereira RH, Folescu TW, Albano RM, Santos EA, Junior LG, Marques EA.
J Cyst Fibros. 2011;10(2):140-2.
KPC-2 carbapenemase-producing Klebsiella pneumoniae isolates from patients with Cystic Fibrosis.
21220216
 FEMALE Young Adult
KPC-2 carbapenemase-producing Klebsiella pneumoniae isolates from patients with Cystic Fibrosis.
Leao RS, Pereira RH, Folescu TW, Albano RM, Santos EA, Junior LG, Marques EA.
J Cyst Fibros. 2011;10(2):140-2.
KPCs enzyme are plasmid-borne and can accumulate and transfer resistance determinants to other classes of antibiotics.We report two cases of KPC-2 carbapenemase-producing Klebsiella pneumoniae isolates from Cystic Fibrosis patients.
21955974
 MIXED_SAMPLE Young Adult
Nebulized tobramycin: prevention of pneumonias in patients with severe cerebral palsy.
Plioplys AV, Kasnicka I.
J Pediatr Rehabil Med. 2011;4(2):155-8.
As in cystic fibrosis patients, patients with severe cerebral palsy may benefit from the intermittent use of nebulized tobramycin to prevent pneumonias and hospitalizations due to pneumonia.
21955974
 MIXED_SAMPLE Young Adult
Nebulized tobramycin: prevention of pneumonias in patients with severe cerebral palsy.
Plioplys AV, Kasnicka I.
J Pediatr Rehabil Med. 2011;4(2):155-8.
As in cystic fibrosis patients, patients with severe cerebral palsy may benefit from the intermittent use of nebulized tobramycin to prevent pneumonias and hospitalizations due to pneumonia.
21955974
 MIXED_SAMPLE Young Adult
Nebulized tobramycin: prevention of pneumonias in patients with severe cerebral palsy.
Plioplys AV, Kasnicka I.
J Pediatr Rehabil Med. 2011;4(2):155-8.
Nebulized tobramycin has been shown to be effective in preventing pneumonias, and in improving lung function in cystic fibrosis patients.
20658485
 MIXED_SAMPLE Infant
Inhaled colistin for the treatment of tracheobronchitis and pneumonia in critically ill children without cystic fibrosis.
Falagas ME, Sideri G, Korbila IP, Vouloumanou EK, Papadatos JH, Kafetzis DA.
Pediatr Pulmonol. 2010;45(11):1135-40.
Inhaled colistin for the treatment of tracheobronchitis and pneumonia in critically ill children without cystic fibrosis.
19347677
 MALE Child
Air filled, inflammatory, lung pseudo-cyst: etio-pathogenesis and management.
Jetley NK, El-Wahed Hussein MR, Softha AL.
Indian J Pediatr. 2009;76(3):324-6.
Necrotising pneumonias, trauma, cystic fibrosis and kerosene poisoning may be the cause of acquired cysts in the lungs during childhood.
19656976
 OTHER
Trichosporon mycotoxinivorans, a novel respiratory pathogen in patients with cystic fibrosis.
Hickey PW, Sutton DA, Fothergill AW, Rinaldi MG, Wickes BL, Schmidt HJ, Walsh TJ.
J Clin Microbiol. 2009;47(10):3091-7.
The index patient died with histologically documented Trichosporon pneumonia complicating cystic fibrosis.
19061488
(2628933)
 OTHER
First isolation of two colistin-resistant emerging pathogens, Brevundimonas diminuta and Ochrobactrum anthropi, in a woman with cystic fibrosis: a case report.
Menuet M, Bittar F, Stremler N, Dubus JC, Sarles J, Raoult D, Rolain JM.
J Med Case Rep. 2008;2:373.
We report the isolation and identification, by 16S rRNA amplification and sequencing, of two emerging pathogens resistant to colistin, Brevundimonas diminuta and Ochrobactrum anthropi, in a 17-year-old woman with cystic fibrosis and pneumonia.