Cystic fibrosis

Cystic fibrosis (CF) is a genetic disorder characterized by the production of sweat with a high salt content and mucus secretions with an abnormal viscosity.

Pulmonary fibrosis

Replacement of normal lung tissues by fibroblasts and collagen.


Total: 4

                       


(per page)
PMID (PMCID)
26855654
(4735539)
 OTHER
Single lung transplantation in a patient with retrospective positive cross-match.
Lesinska AJ, Piotrowska M, Dec P, Wasilewski P, Kubisa A, Pierog J, Wojcik N, Czarnecka M, Kubisa B, Grodzki T.
Kardiochir Torakochirurgia Pol. 2015;12(4):351-4.
Lung transplantation is a method useful in such non-malignant end-stage parenchymal and vascular diseases as: chronic obstructive pulmonary disease (COPD), idiopathic interstitial pulmonary fibrosis, cystic fibrosis, or primary pulmonary hypertension.
25588765
 OTHER Adult
Low-flow veno-venous extracorporeal CO2 removal: first clinical experience in lung transplant recipients.
Ruberto F, Bergantino B, Testa MC, D'Arena C, Bernardinetti M, Diso D, De Giacomo T, Venuta F, Pugliese F.
Int J Artif Organs. 2014;37(12):911-7.
Two patients with cystic fibrosis, one with pulmonary fibrosis, and one with emphysema were included.
16143243
 MIXED_SAMPLE Adult
Upper lobe fibrosis: a novel manifestation of chronic allograft dysfunction in lung transplantation.
Pakhale SS, Hadjiliadis D, Howell DN, Palmer SM, Gutierrez C, Waddell TK, Chaparro C, Davis RD, Keshavjee S, Hutcheon MA, Singer LG.
J Heart Lung Transplant. 2005;24(9):1260-8.
Primary diagnoses were cystic fibrosis, 6; emphysema, 4; sarcoidosis, 1; and pulmonary fibrosis, 2 patients.
714533
 FEMALE
Childhood sarcoidosis with fatal cor pulmonale.
Moffat RE, Sobonya RE, Chang CH.
Pediatr Radiol. 1978;7(3):180-2.
Chest radiographs demonstrated marked pulmonary fibrosis without the changes of severe bronchiectasis that would be anticipated with cystic fibrosis.