Cystic fibrosis

Cystic fibrosis (CF) is a genetic disorder characterized by the production of sweat with a high salt content and mucus secretions with an abnormal viscosity.

Respiratory failure

A severe form of respiratory insufficiency characterized by inadequate gas exchange such that the levels of oxygen or carbon dioxide cannot be maintained within normal limits.


Total: 35

                       


(per page)
PMID (PMCID)
29742226
(5885241)
 MALE Adult
Influenza A non-H1N1 associated with acute respiratory failure and acute renal failure in a previously vaccinated cystic fibrosis patient.
Penteado LP, Osorio CS, Balbinotto A, Dalcin PTR.
Rev Bras Ter Intensiva. 2018;30(1):127-130.
Influenza A non-H1N1 associated with acute respiratory failure and acute renal failure in a previously vaccinated cystic fibrosis patient.
28964265
(5623063)
 MALE Young Adult
Incidental late diagnosis of cystic fibrosis following AH1N1 influenza virus pneumonia: a case report.
Iadevaia C, Iacotucci P, Carnovale V, Calabrese C, Rea G, Ferrara N, Perrotta F, Mazzarella G, Bianco A.
J Med Case Rep. 2017;11(1):278.
We report a case of late incidental cystic fibrosis diagnosis in a young Caucasian man suffering from respiratory failure following infection due to AH1N1 influenza virus.
27080707
 FEMALE Adult
Long-term leukopenia in a lung transplanted patient with cystic fibrosis treated with zoledronic acid: a case report.
Karahasanovic A, Thorsteinsson AL, Bjarnason NH, Eiken P.
Osteoporos Int. 2016;27(8):2621-5.
Cystic fibrosis (CF) is a serious autosomal recessive genetic disorder associated with chronic lung disease, malabsorption, malnutrition, pancreatic insufficiency and premature respiratory failure.
26445233
(4596362)
 MALE Child
A case of failed eradication of cystic fibrosis-related sinus colonisation by Pseudomonas aeruginosa.
Linnane B, Kearse L, O'Connell NH, Fenton J, Kiernan MG, Dunne CP.
BMC Pulm Med. 2015;15:114.
Pseudomonas aeruginosa is a pathogen associated with cystic fibrosis that has potential to decrease lung function and cause respiratory failure.
25705310
 OTHER
Allergic bronchopulmonary aspergillosis in patient with cystic fibrosis - a case report.
Ionescu MD, Balgradean M, Marcu V.
Maedica (Buchar). 2014;9(4):387-90.
We present the case of a 14 - year- old female teenager with cystic fibrosis (CF), admitted in our hospital with respiratory failure and persistent cyanosis.
24846285
 FEMALE Young Adult
Extracorporeal membrane oxygenation (ECMO) in cystic fibrosis.
Shah N, Perrin F.
Paediatr Respir Rev. 2014;15 Suppl 1:26-8.
We discuss this form of treatment, particularly in relation to respiratory failure secondary to influenza in a patient with cystic fibrosis whose condition deteriorated post partum.
25299375
 FEMALE Young Adult
Lung transplant for a patient with cystic fibrosis and active Burkholderia Cenocepacia pneumonia.
Salizzoni S, Pilewski J, Toyoda Y.
Exp Clin Transplant. 2014;12(5):487-9.
A 24-year-old white woman who had cystic fibrosis presented with respiratory failure caused by B. Cenocepacia pneumonia.
23453545
 MALE Infant, Newborn
The use of continuous positive airway pressure or non-invasive ventilation as forms of respiratory support in children with cystic fibrosis.
Armstrong D.
Paediatr Respir Rev. 2013;14 Suppl 1:19-21.
Non-invasive ventilation is used in patients with cystic fibrosis to treat respiratory failure, as a bridge to transplantation and as an adjunct to airway clearance techniques, despite a limited evidence base, particularly amongst the paediatric population.
22266831
 FEMALE Infant, Newborn
Cystic fibrosis: an unusual neonatal presentation.
Sankaran K, Kalapurackal M, Wiebe S.
Pediatr Pulmonol. 2012;47(6):620-2.
In this report we describe a neonate born with cystic fibrosis (CF) who presented to us with hypoxic respiratory failure, pulmonary hypertension, and hypercarbia without lactic acedemia from sticky mucous plugging and massive lung collapse.
21620114
 MALE Adult
Severe mixed sleep apnea after bilateral lung transplantation in a cystic fibrosis patient: a case report.
Kunos L, Kovats Z, Murakozy G, Sutto Z, Bohacs A, Czebe K, Lang G, Renyi-Vamos F, Klepetko W, Muller V.
Transplant Proc. 2011;43(4):1292-3.
Herein we have reported a case of a 35-year-old man undergoing bilateral lung transplantation owing to worsening of chronic respiratory failure from cystic fibrosis.
20133415
 FEMALE Adult
Empyema due to a highly transmissible Pseudomonas aeruginosa strain in an adult cystic fibrosis patient.
Mohan K, Lakshman V, Fothergill JL, Ledson MJ, Winstanley C, Walshaw MJ.
J Med Microbiol. 2010;59(Pt 5):614-6.
Chronic pulmonary infection with Pseudomonas aeruginosa occurs in up to 85 % of individuals with cystic fibrosis (CF) by the time they reach adulthood, and is the major cause of morbidity and mortality: nearly all patients die from progressive respiratory failure due to repeated pulmonary exacerbations.
19020061
 MALE Adult
Acute respiratory failure involving an R variant of Mycobacterium abscessus.
Catherinot E, Roux AL, Macheras E, Hubert D, Matmar M, Dannhoffer L, Chinet T, Morand P, Poyart C, Heym B, Rottman M, Gaillard JL, Herrmann JL.
J Clin Microbiol. 2009;47(1):271-4.
We report the case of a cystic fibrosis patient colonized with a smooth-morphotype form of Mycobacterium abscessus who developed acute respiratory failure with the emergence of an isogenic rough (R) variant while he was recovering from peritonitis-induced shock.
19656132
 MALE Middle Aged
Successful lung transplantation in an HIV- and HBV-positive patient with cystic fibrosis.
Bertani A, Grossi P, Vitulo P, D'Ancona G, Arcadipane A, Nanni Costa A, Gridelli B.
Am J Transplant. 2009;9(9):2190-6.
The results of a double lung transplant performed in an HIV and HBV co-infected patient with cystic fibrosis (CF) and end-stage respiratory failure (ESRF) are presented after a 2-year follow-up.
19010214
 MALE
Combined lung and liver transplantation-University Hospital Reina Sofia experience: two case reports.
Moreno Casado P, Alvarez Kindelan A, Algar Algar FJ, Espinosa Jimenez D, Cano Garcia JR, Cerezo Madueno F, Baamonde Laborda C, Lopez Cillero P, Salvatierra Velazquez A.
Transplant Proc. 2008;40(9):3126-7.
We performed two combined lung and liver transplantations for patients with cystic fibrosis with chronic respiratory failure accompanied by advanced liver disease.
17550621
(1899497)
 MALE Middle Aged
Extracorporeal membrane oxygenator as a bridge to successful surgical repair of bronchopleural fistula following bilateral sequential lung transplantation: a case report and review of literature.
Khan NU, Al-Aloul M, Khasati N, Machaal A, Leonard CT, Yonan N.
J Cardiothorac Surg. 2007;2:28.
Lung transplantation (LTx) is widely accepted as a therapeutic option for end-stage respiratory failure in cystic fibrosis.
17550621
(1899497)
 MALE Middle Aged
Extracorporeal membrane oxygenator as a bridge to successful surgical repair of bronchopleural fistula following bilateral sequential lung transplantation: a case report and review of literature.
Khan NU, Al-Aloul M, Khasati N, Machaal A, Leonard CT, Yonan N.
J Cardiothorac Surg. 2007;2:28.
A 47-year-old man with end-stage respiratory failure due to cystic fibrosis underwent bilateral sequential lung transplantation.
16886689
 FEMALE
[Delirium in critically ill children in a paediatric intensive care unit].
Schieveld JN, Leroy PL, Leentjens AF.
Ned Tijdschr Geneeskd. 2006;150(28):1545-8.
The second child, admitted due to an exacerbation of cystic fibrosis with the threat of respiratory failure, suffered from hypoactive delirium with regression, inconsolability, dyspraxia and dysphasia.
15865595
 MALE Child
Life-threatening allergic bronchopulmonary aspergillosis in a well child with cystic fibrosis.
Skowronski E, Fitzgerald DA.
Med J Aust. 2005;182(9):482-3.
We report a well 8-year-old boy with cystic fibrosis and normal lung function who progressed to respiratory failure over several days, attributable to ABPA.
15601277
 FEMALE Adult
Management of a parturient with respiratory failure secondary to cystic fibrosis.
Cameron AJ, Skinner TA.
Anaesthesia. 2005;60(1):77-80.
Management of a parturient with respiratory failure secondary to cystic fibrosis.
15601277
 FEMALE Adult
Management of a parturient with respiratory failure secondary to cystic fibrosis.
Cameron AJ, Skinner TA.
Anaesthesia. 2005;60(1):77-80.
A 21-year-old with end-stage respiratory failure and cor pulmonale due to cystic fibrosis became pregnant.