Cystic fibrosis

Cystic fibrosis (CF) is a genetic disorder characterized by the production of sweat with a high salt content and mucus secretions with an abnormal viscosity.

Metabolic alkalosis



Total: 25

                       


(per page)
PMID (PMCID)
31183080
 OTHER
Pseudo-Bartter syndrome in children with cystic fibrosis.
Faraji-Goodarzi M.
Clin Case Rep. 2019;7(6):1123-1126.
We report a case of a boy aged 4.5 years with cystic fibrosis, presenting under-weightness, hypocalcemia, metabolic alkalosis, hypokalemia, and hyponatremia.
24821548
 MALE Child
Episodic seasonal Pseudo-Bartter syndrome in cystic fibrosis.
Kintu B, Brightwell A.
Paediatr Respir Rev. 2014;15 Suppl 1:19-21.
Pseudo-Bartter syndrome (PBS) describes an uncommon but well recognised complication of cystic fibrosis leading to hypochloraemic, hypokalaemic metabolic alkalosis.
19030645
 MALE Infant
[Dehydration and metabolic alkalosis: an unusual presentation of cystic fibrosis in an infant].
Aranzamendi RJ, Breitman F, Asciutto C, Delgado N, Castanos C.
Arch Argent Pediatr. 2008;106(5):443-6.
[Dehydration and metabolic alkalosis: an unusual presentation of cystic fibrosis in an infant].
17479655
 FEMALE Infant
Modified oral rehydration therapy in a case with cystic fibrosis.
Yalcin SS, Akca T, Genc O, Celik M, Dogru D, Ozcelik U.
Turk J Pediatr. 2007;49(1):102-4.
Infants with cystic fibrosis can develop episodes of hyponatremic, hypochloremic dehydration with metabolic alkalosis, and management is difficult.
15823195
 MALE Adult
Clinical presentation of metabolic alkalosis in an adult patient with cystic fibrosis.
Sweetser LJ, Douglas JA, Riha RL, Bell SC.
Respirology. 2005;10(2):254-6.
An adult cystic fibrosis patient who presented with a severe respiratory exacerbation accompanied by metabolic alkalosis is presented and the effects of volume correction are reported.
15823195
 MALE Adult
Clinical presentation of metabolic alkalosis in an adult patient with cystic fibrosis.
Sweetser LJ, Douglas JA, Riha RL, Bell SC.
Respirology. 2005;10(2):254-6.
Clinical presentation of metabolic alkalosis in an adult patient with cystic fibrosis.
15463898
 MALE Infant
Cystic fibrosis presenting as metabolic alkalosis in a boy with the rare D579G mutation.
Salvatore D, Tomaiuolo R, Abate R, Vanacore B, Manieri S, Mirauda MP, Scavone A, Schiavo MV, Castaldo G, Salvatore F.
J Cyst Fibros. 2004;3(2):135-6.
Cystic fibrosis presenting as metabolic alkalosis in a boy with the rare D579G mutation.
10719683
 MALE Infant
[Turkish infant with hypoelectrolytemia and metabolic alkalosis as the sole manifestations of a mild form of cystic fibrosis (mutation D110H)].
Weller F, Wiebicke W, Tummler B.
Klin Padiatr. 2000;212(1):41-3.
We report the history of an infant who presented with hypotonic dehydration and metabolic alkalosis, in whom the diagnosis of cystic fibrosis was made on the basis of investigations for rare cystic fibrosis mutations.
10719683
 MALE Infant
[Turkish infant with hypoelectrolytemia and metabolic alkalosis as the sole manifestations of a mild form of cystic fibrosis (mutation D110H)].
Weller F, Wiebicke W, Tummler B.
Klin Padiatr. 2000;212(1):41-3.
We report the history of an infant who presented with hypotonic dehydration and metabolic alkalosis, in whom the diagnosis of cystic fibrosis was made on the basis of investigations for rare cystic fibrosis mutations.
10719683
 MALE Infant
[Turkish infant with hypoelectrolytemia and metabolic alkalosis as the sole manifestations of a mild form of cystic fibrosis (mutation D110H)].
Weller F, Wiebicke W, Tummler B.
Klin Padiatr. 2000;212(1):41-3.
A mild variant of cystic fibrosis has to be considered in infants presenting with unexplained hypoelectrolytemia and metabolic alkalosis.
10719683
 MALE Infant
[Turkish infant with hypoelectrolytemia and metabolic alkalosis as the sole manifestations of a mild form of cystic fibrosis (mutation D110H)].
Weller F, Wiebicke W, Tummler B.
Klin Padiatr. 2000;212(1):41-3.
[Turkish infant with hypoelectrolytemia and metabolic alkalosis as the sole manifestations of a mild form of cystic fibrosis (mutation D110H)].
9048354
 MALE
Cystic fibrosis presenting with hypokalemia and metabolic alkalosis in a previously healthy adolescent.
Bates CM, Baum M, Quigley R.
J Am Soc Nephrol. 1997;8(2):352-5.
Cystic fibrosis presenting with hypokalemia and metabolic alkalosis in a previously healthy adolescent.
8087218
 MIXED_SAMPLE Infant, Newborn
[Cystic fibrosis revealed by dehydration with hypochloronatremic alkalosis in 3 infants and a neonate].
Berard E, Maillotte AM, Albertini M, Delalandre E, Boutte P, Mariani R.
Arch Pediatr. 1994;1(1):42-5.
CONCLUSION--Metabolic alkalosis with hypochloronatremia plus progressive, severe dehydration in infants whose diuresis is paradoxically normal must be followed by examination for cystic fibrosis.
8087218
 MIXED_SAMPLE Infant, Newborn
[Cystic fibrosis revealed by dehydration with hypochloronatremic alkalosis in 3 infants and a neonate].
Berard E, Maillotte AM, Albertini M, Delalandre E, Boutte P, Mariani R.
Arch Pediatr. 1994;1(1):42-5.
BACKGROUND--Acute dehydration with hypochloronatremic metabolic alkalosis is a classical complication of cystic fibrosis of the pancreas.
1915522
 FEMALE Infant
Chronic metabolic alkalosis in an infant with cystic fibrosis.
Eigenmann P, Deleze G, Kuchler H.
Eur J Pediatr. 1991;150(9):669-70.
Chronic metabolic alkalosis in an infant with cystic fibrosis.
1903109
 MALE Infant
Cystic fibrosis presenting with recurrent vomiting and metabolic alkalosis.
Mathew PM, Hamdan JA, Nazer H.
Eur J Pediatr. 1991;150(4):264-6.
Cystic fibrosis presenting with recurrent vomiting and metabolic alkalosis.
2921995
 FEMALE Child
[Respiratory insufficiency in mucoviscidosis. Pathophysiologic aspects of conservative drug therapy].
Storm W.
Monatsschr Kinderheilkd. 1989;137(1):52-3.
The compensated chronic respiratory acidosis in a girl with cystic fibrosis changed into a mixed respiratory acidosis and metabolic alkalosis under the influence of therapeutic measures.
7146884
 MALE Infant
Cystic fibrosis presenting with chronic electrolyte depletion, metabolic alkalosis and hyperaldosteronism.
Forsyth JS, Gillies DR, Wilson SG.
Scott Med J. 1982;27(4):333-5.
Cystic fibrosis presenting with chronic electrolyte depletion, metabolic alkalosis and hyperaldosteronism.
7075099
 MIXED_SAMPLE Infant
Hypoelectrolytemia as a presentation and complication of cystic fibrosis.
Ruddy R, Anolik R, Scanlin TF.
Clin Pediatr (Phila). 1982;21(6):367-9.
We describe three patients with cystic fibrosis (CF) with four episodes of hypoelectrolytemia, two of which were associated with documented metabolic alkalosis.
440868
 MIXED_SAMPLE Infant
Hypoelectrolytemia and metabolic alkalosis in infants with cystic fibrosis.
Beckerman RC, Taussig LM.
Pediatrics. 1979;63(4):580-3.
The lack of shock and hyperpyrexia together with the apparent chronicity of electrolyte losses differentiates metabolic alkalosis from the heat prostration syndrome, a more acute complication of cystic fibrosis.