Neuroblastoma

Neuroblastoma is a malignant tumor of neural crest cells, the cells that give rise to the sympathetic nervous system, which is observed in children.

Total colonic aganglionosis

A type of aganglionic megacolon in which the aganglionic segment comprises the entire colon.


Total: 2

                       


(per page)
PMID (PMCID)
7472988
 FEMALE Infant, Newborn
The complete spectrum of neurocristopathy in an infant with congenital hypoventilation, Hirschsprung's disease, and neuroblastoma.
Stovroff M, Dykes F, Teague WG.
J Pediatr Surg. 1995;30(8):1218-21.
Their combined occurrence in a newborn infant presenting with total colonic aganglionosis, central hypoventilation, and multifocal neuroblastoma had not been reported previously.
3430302
 MALE Infant, Newborn
Total colonic aganglionosis (Zuelzer-Wilson syndrome) and congenital failure of automatic control of ventilation (Ondine's curse).
O'Dell K, Staren E, Bassuk A.
J Pediatr Surg. 1987;22(11):1019-20.
The relevant literature regarding the association of these syndromes, the reversal of male to female predominance in total colonic aganglionosis v Hirschsprung's disease, their association with pheochromocytoma and neuroblastoma, and the possible etiologic role of cessation of neural crest cell migration, are discussed.