Monomelic amyotrophy

Monomelic amyotrophy (MA) is a rare benign lower motor neuron disorder characterized by muscular weakness and wasting in the distal upper extremities during adolescence followed by a spontaneous halt in progression and a stabilization of symptoms.

Muscle weakness

Reduced strength of muscles.


Total: 2

                      


(per page)
PMID (PMCID)
27550499
(4999413)
MALE Adult
Hirayama Disease with Proximal Involvement.
Kim J, Kim Y, Kim S, Oh K.
J Korean Med Sci. 2016;31(10):1664-7.
He was diagnosed with Hirayama disease 9 years ago, while there was no further progression of the muscle weakness afterward.
21344999
MALE Middle Aged
Monomelic amyotrophy is not always benign: a case report.
Moglia C, Calvo A, Cammarosano S, Ilardi A, Canosa A, Gallo S, Bersano E, Chio A.
Amyotroph Lateral Scler. 2011;12(4):307-8.
Monomelic amyotrophy (MA) is a variant of motor neuron disease (MND), characterized by muscle weakness and atrophy restricted to one limb.