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Polycythemia vera

Polycythemia vera (PV) is an acquired myeloproliferative disorder characterized by an elevated absolute red blood cell mass caused by uncontrolled red blood cell production, frequently associated with uncontrolled white blood cell and platelet production.

Extramedullary hematopoiesis

The process of hematopoiesis occurring outside of the bone marrow (in the liver, thymus, and spleen) in the postnatal organisms.

Total: 17

(per page)

PMID (PMCID)
28133558 (5241451)	OTHER
	Myelopathy due to Spinal Extramedullary Hematopoiesis in a Patient with Polycythemia Vera.
	Ito S, Fujita N, Hosogane N, Nagoshi N, Yagi M, Iwanami A, Watanabe K, Tsuji T, Nakamura M, Matsumoto M, Ishii K. Case Rep Orthop. 2017;2017:2416365.
	Myelopathy due to Spinal Extramedullary Hematopoiesis in a Patient with Polycythemia Vera.
24348604 (3857981)	OTHER
	Paraspinal and presacral extramedullary hematopoiesis: a rare manifestation of polycythemia vera.
	Ahmad K, Ansari S, Koirala R, Agarwal M, Chaudhary S. Iran J Radiol. 2013;10(3):164-8.
	Paraspinal and presacral extramedullary hematopoiesis: a rare manifestation of polycythemia vera.
24348604 (3857981)	OTHER
	Paraspinal and presacral extramedullary hematopoiesis: a rare manifestation of polycythemia vera.
	Ahmad K, Ansari S, Koirala R, Agarwal M, Chaudhary S. Iran J Radiol. 2013;10(3):164-8.
	We report a case of a 38-year-old female with paraspinal and presacral extramedullary hematopoiesis with polycythemia vera.
20013324	FEMALE
	Activated STAT1 and STAT5 transcription factors in extramedullary hematopoietic tissue in a polycythemia vera patient carrying the JAK2 V617F mutation.
	Meyer T, Ruppert V, Gorg C, Neubauer A. Int J Hematol. 2010;91(1):117-20.
	Our data suggest that dysregulated STAT signal pathways are engaged in extramedullary hematopoiesis in polycythemia vera.
20013324	FEMALE
	Activated STAT1 and STAT5 transcription factors in extramedullary hematopoietic tissue in a polycythemia vera patient carrying the JAK2 V617F mutation.
	Meyer T, Ruppert V, Gorg C, Neubauer A. Int J Hematol. 2010;91(1):117-20.
	Here, we report on a 76-year-old female patient presenting with JAK2V617F-positive polycythemia vera and a pelvic mass with extramedullary hematopoiesis.
20661915	MIXED_SAMPLE	Adult
	Effective management of accelerated phase myelofibrosis with low-dose splenic radiotherapy.
	Pardanani A, Brown P, Neben-Wittich M, Tobin R, Tefferi A. Am J Hematol. 2010;85(9):715-6.
	The main cause of hepatosplenomegaly in primary (PMF), post polycythemia vera (post-PV MF), and post essential thrombocythemia (post-ET MF) myelofibrosis (MF) is extramedullary hematopoiesis (EMH).
17109152	MALE
	Synovial tumefactive extramedullary hematopoiesis associated to polycythemia vera.
	Alvarez-Arguelles Cabrera H, Carrasco Juan JL, Garcia Castro MC, Gonzalez Gaitano M, Bonilla Arjona A, Diaz-Flores L. Virchows Arch. 2007;450(1):109-13.
	Synovial tumefactive extramedullary hematopoiesis associated to polycythemia vera.
17109152	MALE
	Synovial tumefactive extramedullary hematopoiesis associated to polycythemia vera.
	Alvarez-Arguelles Cabrera H, Carrasco Juan JL, Garcia Castro MC, Gonzalez Gaitano M, Bonilla Arjona A, Diaz-Flores L. Virchows Arch. 2007;450(1):109-13.
	The case of a 66-year-old male patient with a chronic myeloproliferative type polycythemia vera disorder, who after 2 years of evolution is developing a tumefactive extramedullary hematopoiesis (TEH) located in the synovial of the articulation in the right knee, is described.
11902077	FEMALE
	Spinal cord compression due to extramedullary hematopoiesis associated with polycythemia vera--case report.
	Ohta Y, Shichinohe H, Nagashima K. Neurol Med Chir (Tokyo). 2002;42(1):40-3.
	Extramedullary hematopoiesis occurs in patients with various hematologic disorders involving a chronic increase in the production of red blood cells, and is often associated with thalassemia, but is less common with polycythemia vera.
11902077	FEMALE
	Spinal cord compression due to extramedullary hematopoiesis associated with polycythemia vera--case report.
	Ohta Y, Shichinohe H, Nagashima K. Neurol Med Chir (Tokyo). 2002;42(1):40-3.
	Considering the possibility of central nervous system extramedullary hematopoiesis in patients with polycythemia vera, an early diagnosis is necessary for a favorable prognosis.
11426569	FEMALE
	Subcutaneous extramedullary hematopoiesis in a patient with secondary myelofibrosis following polycythemia vera.
	Tanaka M, Kanamori H, Yamaji S, Mishima A, Yamazaki E, Taguchi J, Aoba M, Fujisawa S, Mohri H, Ishigatsubo Y. Leuk Lymphoma. 2001;40(3-4):437-40.
	Although extramedullary hematopoiesis has been generally observed in primary myelofibrosis, in this case it was seen in myelofibrosis secondary to polycythemia vera.
11426569	FEMALE
	Subcutaneous extramedullary hematopoiesis in a patient with secondary myelofibrosis following polycythemia vera.
	Tanaka M, Kanamori H, Yamaji S, Mishima A, Yamazaki E, Taguchi J, Aoba M, Fujisawa S, Mohri H, Ishigatsubo Y. Leuk Lymphoma. 2001;40(3-4):437-40.
	Subcutaneous extramedullary hematopoiesis in a patient with secondary myelofibrosis following polycythemia vera.
10931988	FEMALE
	MR imaging of focal splenic extramedullary hematopoiesis in polycythemia vera: case report.
	Gabata T, Kadoya M, Mori A, Kobayashi S, Sanada J, Matsui O. Abdom Imaging. 2000;25(5):514-6.
	MR imaging of focal splenic extramedullary hematopoiesis in polycythemia vera: case report.
8922492	MALE	Middle Aged
	Spinal cord compression due to extramedullary hematopoiesis in the proliferative phase of polycythemia vera.
	de Morais JC, Spector N, Lavrado FP, Nobre LF, de Mattos JP, Pulcheri W, Nucci M, Novis S, de Oliveira HP. Acta Haematol. 1996;96(4):242-4.
	The association of extramedullary hematopoiesis with polycythemia vera in the proliferative phase is much less usual.
8922492	MALE	Middle Aged
	Spinal cord compression due to extramedullary hematopoiesis in the proliferative phase of polycythemia vera.
	de Morais JC, Spector N, Lavrado FP, Nobre LF, de Mattos JP, Pulcheri W, Nucci M, Novis S, de Oliveira HP. Acta Haematol. 1996;96(4):242-4.
	Spinal cord compression due to extramedullary hematopoiesis in the proliferative phase of polycythemia vera.
2595427	MALE	Middle Aged
	Intracranial granulocytic sarcoma in postpolycythemia myeloid metaplasia.
	Roy EP 3rd, Rogers JS 2nd, Riggs JE. South Med J. 1989;82(12):1564-7.
	A 57-year-old man with a ten-year history of polycythemia vera had myeloid metaplasia, extramedullary hematopoiesis, and terminally, possible leukemic transformation with intracranial granulocytic sarcoma.
7387474	MALE	Adult
	Spinal cord compression with paraplegia in myelofibrosis.
	Oustwani MB, Kurtides ES, Christ M, Ciric I. Arch Neurol. 1980;37(6):389-90.
	Paraplegia developed in a 70-year-old man with a 15-year history of polycythemia rubra vera and a two-year history of myelofibrosis, due to extensive epidural involvement by extramedullary hematopoiesis.