Mixed connective tissue disease

Mixed connective tissue disease (MCTD) is a rare connective tissue disorder combining clinical features of systemic lupus erythematosus (SLE), systemic sclerosis (SSc), polymyositis (PM) (see these terms) and/or rheumatoid arthritis (RA).

Intestinal pseudo-obstruction

A functional rather than mechanical obstruction of the intestines, associated with manifestations that resemble those caused by an intestinal obstruction, including distension, abdominal pain, nausea, vomiting, constipation or diarrhea, in an individual in whom a mechanical blockage has been excluded.


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(per page)
PMID (PMCID)
1436269
FEMALE Adult
Pneumatosis intestinalis in mixed connective tissue disease.
van Leeuwen JC, Nossent JC.
Neth J Med. 1992;40(5-6):299-304.
Two young female patients with established mixed connective tissue disease (MCTD) are described, in whom the disease course was complicated by intestinal pseudo-obstruction and pneumoperitoneum due to pneumatosis intestinalis.