Hereditary spherocytosis

Hereditary spherocytosis is a congenital hemolytic anemia with a wide clinical spectrum (from symptom-free carriers to severe hemolysis) characterized by anemia, variable jaundice, splenomegaly and cholelithiasis.

Hypertension

The presence of chronic increased pressure in the systemic arterial system.


Total: 4

                       


(per page)
PMID (PMCID)
26009599
 FEMALE Child
Malignant systemic hypertension, encephalopathy and bradycardia following splenectomy for hereditary spherocytosis.
Varshney A, Sharma S, Dey S, Gupta DK.
BMJ Case Rep. 2015;2015:.
Malignant systemic hypertension, encephalopathy and bradycardia following splenectomy for hereditary spherocytosis.
1936235
 MALE Middle Aged
Spherocytosis and pulmonary hypertension coincidental occurrence or causal relationship?
Verresen D, De Backer W, Van Meerbeeck J, Neetens I, Van Marck E, Vermeire P.
Eur Respir J. 1991;4(5):629-31.
A report is given on a 59 yr old man with hereditary spherocytosis and progressive shortness of breath on exertion, due to severe pulmonary hypertension and cor pulmonale.
1936235
 MALE Middle Aged
Spherocytosis and pulmonary hypertension coincidental occurrence or causal relationship?
Verresen D, De Backer W, Van Meerbeeck J, Neetens I, Van Marck E, Vermeire P.
Eur Respir J. 1991;4(5):629-31.
Both primary pulmonary hypertension and hereditary spherocytosis have a low incidence in the general population and their simultaneous occurrence has not been reported previously; the possibility that this was due to a causal relationship and not to coincidence cannot be ruled out, in view of some similarities with pulmonary hypertension complicating sickle cell anaemia.
1936235
 MALE Middle Aged
Spherocytosis and pulmonary hypertension coincidental occurrence or causal relationship?
Verresen D, De Backer W, Van Meerbeeck J, Neetens I, Van Marck E, Vermeire P.
Eur Respir J. 1991;4(5):629-31.
Both primary pulmonary hypertension and hereditary spherocytosis have a low incidence in the general population and their simultaneous occurrence has not been reported previously; the possibility that this was due to a causal relationship and not to coincidence cannot be ruled out, in view of some similarities with pulmonary hypertension complicating sickle cell anaemia.