Hereditary spherocytosis

Hereditary spherocytosis is a congenital hemolytic anemia with a wide clinical spectrum (from symptom-free carriers to severe hemolysis) characterized by anemia, variable jaundice, splenomegaly and cholelithiasis.

Myelofibrosis

Replacement of bone marrow by fibrous tissue.


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(per page)
PMID (PMCID)
19046318
 MIXED_SAMPLE Adult
Effect of hydroxyurea on extramedullary haematopoiesis in thalassaemia intermedia: case reports and literature review.
Meo A, Cassinerio E, Castelli R, Bignamini D, Perego L, Cappellini MD.
Int J Lab Hematol. 2008;30(5):425-31.
Extramedullary haematopoiesis (EH) is the production of blood cell precursors outside the bone marrow that occurs in various disorders, such as thalassaemia, sickle cell anaemia, hereditary spherocytosis, polycythaemia vera, myelofibrosis and other haematological diseases.
8922492
 MALE Middle Aged
Spinal cord compression due to extramedullary hematopoiesis in the proliferative phase of polycythemia vera.
de Morais JC, Spector N, Lavrado FP, Nobre LF, de Mattos JP, Pulcheri W, Nucci M, Novis S, de Oliveira HP.
Acta Haematol. 1996;96(4):242-4.
Extramedullary hematopoiesis is a common accompaniment of a variety of hematologic diseases such as hereditary spherocytosis, thalassemia and myelofibrosis.