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Hereditary spherocytosis

Hereditary spherocytosis is a congenital hemolytic anemia with a wide clinical spectrum (from symptom-free carriers to severe hemolysis) characterized by anemia, variable jaundice, splenomegaly and cholelithiasis.

Sepsis

Systemic inflammatory response to infection.

Total: 4

(per page)

PMID (PMCID)
10602897	MIXED_SAMPLE	Adult
	Frequency of very late fatal sepsis after splenectomy for hereditary spherocytosis: impact of insufficient antibody response to pneumococcal infection.
	Eber SW, Langendorfer CM, Ditzig M, Reinhardt D, Stohr G, Soldan W, Schroter W, Tchernia G. Ann Hematol. 1999;78(11):524-8.
	Within the past 7 years we have learned of four cases of sepsis or meningitis (three fatal) in adult patients with hereditary spherocytosis who had been splenectomized years earlier.
10602897	MIXED_SAMPLE	Adult
	Frequency of very late fatal sepsis after splenectomy for hereditary spherocytosis: impact of insufficient antibody response to pneumococcal infection.
	Eber SW, Langendorfer CM, Ditzig M, Reinhardt D, Stohr G, Soldan W, Schroter W, Tchernia G. Ann Hematol. 1999;78(11):524-8.
	Very late sepsis in splenectomized patients with hereditary spherocytosis has been seen rarely up to now; the frequency and the immunodeficiency causing it are largely unknown.
10602897	MIXED_SAMPLE	Adult
	Frequency of very late fatal sepsis after splenectomy for hereditary spherocytosis: impact of insufficient antibody response to pneumococcal infection.
	Eber SW, Langendorfer CM, Ditzig M, Reinhardt D, Stohr G, Soldan W, Schroter W, Tchernia G. Ann Hematol. 1999;78(11):524-8.
	Frequency of very late fatal sepsis after splenectomy for hereditary spherocytosis: impact of insufficient antibody response to pneumococcal infection.
3973056	MIXED_SAMPLE	Adult
	Postsplenectomy sepsis 10 years or more after operation.
	Evans DI. J Clin Pathol. 1985;38(3):309-11.
	Three new cases (two fatal) of postsplenectomy sepsis occurring 14, 25, and 26 years after operation for hereditary spherocytosis are described.