Primary myelofibrosis

A rare myeloproliferative neoplasm characterized by stem-cell derived clonal over proliferation of mature myeloid lineages, such as erythrocytes, leukocytes, and megakaryocytes, with variable degrees of megakaryocyte atypia, associated with reticulin and/or collagen bone marrow fibrosis, osteosclerosis, ineffective erythropoiesis, angiogenesis, extramedullary hematopoiesis, and abnormal cytokine expression.

Ascites

Accumulation of fluid in the peritoneal cavity.


Total: 16

                      


(per page)
PMID (PMCID)
27874969
FEMALE
Idiopathic myelofibrosis accompanied by peritoneal extramedullary hematopoiesis presenting as refractory ascites in a dog.
Rautenbach Y, Goddard A, Clift SJ.
Vet Clin Pathol. 2017;46(1):46-53.
This case represents the first report of canine idiopathic myelofibrosis associated with peritoneal extramedullary hematopoiesis, resulting in refractory ascites.
27874969
FEMALE
Idiopathic myelofibrosis accompanied by peritoneal extramedullary hematopoiesis presenting as refractory ascites in a dog.
Rautenbach Y, Goddard A, Clift SJ.
Vet Clin Pathol. 2017;46(1):46-53.
Although idiopathic myelofibrosis is a relatively rare condition in dogs, this case demonstrates that ascites caused by peritoneal implants of hematopoietic tissue may be the initial manifestation of myelofibrosis.
26185644
(4498858)
OTHER
Nontuberculous mycobacterial infection in a patient with myelofibrosis: case report and concise review.
Henriquez-Camacho C, Martinez-Barranco P, Velasco M, Villafuerte-Gutierrez P, Losa J.
Clin Case Rep. 2015;3(6):438-41.
The case describes this unusual infection and highlights the need for additional studies to confirm the etiology of ascites in primary myelofibrosis.
26185644
(4498858)
OTHER
Nontuberculous mycobacterial infection in a patient with myelofibrosis: case report and concise review.
Henriquez-Camacho C, Martinez-Barranco P, Velasco M, Villafuerte-Gutierrez P, Losa J.
Clin Case Rep. 2015;3(6):438-41.
A 70-year-old patient having massive refractory ascites in the course of idiopathic myelofibrosis was diagnosed of peritoneal extramedullary hematopoiesis and developed an overwhelming nontuberculous mycobacterial infection.
25206301
MALE Middle Aged
Intestinal obstruction caused by extramedullary hematopoiesis and ascites in primary myelofibrosis.
Wei XQ, Zheng ZH, Jin Y, Tao J, Abassa KK, Wen ZF, Shao CK, Wei HB, Wu B.
World J Gastroenterol. 2014;20(33):11921-6.
Intestinal obstruction caused by extramedullary hematopoiesis and ascites in primary myelofibrosis.
12857054
FEMALE Middle Aged
Idiopathic myelofibrosis with refractory massive ascites.
Yotsumoto M, Ishida F, Ito T, Ueno M, Kitano K, Kiyosawa K.
Intern Med. 2003;42(6):525-8.
Idiopathic myelofibrosis with refractory massive ascites.
12857054
FEMALE Middle Aged
Idiopathic myelofibrosis with refractory massive ascites.
Yotsumoto M, Ishida F, Ito T, Ueno M, Kitano K, Kiyosawa K.
Intern Med. 2003;42(6):525-8.
A 55-year-old woman presented with massive refractory ascites in the course of idiopathic myelofibrosis.
8503241
FEMALE Middle Aged
Ectopic medullary hematopoiesis as a cause of ascites in agnogenic myeloid metaplasia. Case report and review of the literature.
Knobel B, Melamud E, Virag I, Meytes D.
Acta Haematol. 1993;89(2):104-7.
Ectopic medullary hematopoiesis as a cause of ascites in agnogenic myeloid metaplasia.
1986577
MALE Adult
Ascites revealing peritoneal and hepatic extramedullary hematopoiesis with peliosis in agnogenic myeloid metaplasia: case report and review of the literature.
Liote F, Yeni P, Teillet-Thiebaud F, Barge J, Devars Du Mayne JF, Flamant Y, Molas G, Carbon C.
Am J Med. 1991;90(1):111-7.
A 61-year-old man presented with ascites in the course of agnogenic myeloid metaplasia (AMM).
1986577
MALE Adult
Ascites revealing peritoneal and hepatic extramedullary hematopoiesis with peliosis in agnogenic myeloid metaplasia: case report and review of the literature.
Liote F, Yeni P, Teillet-Thiebaud F, Barge J, Devars Du Mayne JF, Flamant Y, Molas G, Carbon C.
Am J Med. 1991;90(1):111-7.
Ascites revealing peritoneal and hepatic extramedullary hematopoiesis with peliosis in agnogenic myeloid metaplasia: case report and review of the literature.
4014072
FEMALE Middle Aged
Extramedullary hematopoietic ascitic fluid cytology in myelofibrosis.
Silverman JF.
Am J Clin Pathol. 1985;84(1):125-8.
A patient having myelofibrosis with myeloid metaplasia complicated by ascites is reported.
2984361
MALE
Suppression of hepatic hematopoiesis with radioactive gold (198Au).
Turner AR, Gummerman LW, Boggs DR.
J Nucl Med. 1985;26(4):366-7.
A patient with idiopathic myelofibrosis of some 20 yr duration developed esophageal varices and ascites.
6617403
MALE Middle Aged
Ascites progressing to an abdominal mass due to extramedullary hematopoiesis in a patient with agnogenic myeloid metaplasia (AMM).
Marshall JB, Burnett DA, Anderson JC, Zetterman RK.
Dig Dis Sci. 1983;28(10):912-7.
Ascites progressing to an abdominal mass due to extramedullary hematopoiesis in a patient with agnogenic myeloid metaplasia (AMM).
6617403
MALE Middle Aged
Ascites progressing to an abdominal mass due to extramedullary hematopoiesis in a patient with agnogenic myeloid metaplasia (AMM).
Marshall JB, Burnett DA, Anderson JC, Zetterman RK.
Dig Dis Sci. 1983;28(10):912-7.
We report a patient with long-standing agnogenic myeloid metaplasia who developed ascites which progressed over 6 months to a massive solid peritoneal mass as a consequence of intraperitoneal extra-medullary hematopoiesis.
7104962
MALE
Ascites in agnogenic myeloid metaplasia: association with peritoneal implant of myeloid tissue and therapy.
Patel NM, Kurtides ES.
Cancer. 1982;50(6):1189-90.
The case of a patient with agnogenic myeloid metaplasia and myelofibrosis engrafted upon a longstanding treated case of polycythemia rubra vera and presenting with ascites due to peritoneal implants of myeloid tissue is presented.
7104962
MALE
Ascites in agnogenic myeloid metaplasia: association with peritoneal implant of myeloid tissue and therapy.
Patel NM, Kurtides ES.
Cancer. 1982;50(6):1189-90.
Ascites in agnogenic myeloid metaplasia: association with peritoneal implant of myeloid tissue and therapy.