Beta-thalassemia

Beta-thalassemia (BT) is characterized by deficiency (Beta+) or absence (Beta0) of synthesis of the beta globin chains of hemoglobin (Hb).

Extramedullary hematopoiesis

The process of hematopoiesis occurring outside of the bone marrow (in the liver, thymus, and spleen) in the postnatal organisms.


Total: 27

                       


(per page)
PMID (PMCID)
29368108
 MALE
Intracranial Hematopoiesis in Beta Thalassemia: A Case Series.
Merchant R, Choudhari AJ, Verma M, Patkar DP, Doctor P.
Indian J Pediatr. 2018;85(8):679-681.
The authors report two cases of intracranial extramedullary hematopoiesis in beta thalassemia.
28483223
 MALE Child
Temporal bone extramedullary hematopoiesis as a causeof pediatric bilateral conductive hearing loss:Case report and review of the literature.
Lanigan A, Fordham MT.
Int J Pediatr Otorhinolaryngol. 2017;97:135-138.
We report a case of a nine-year-old with beta thalassemia and temporal bone extramedullary hematopoiesis causing ossicular fixation and bilateral conductive hearing loss.
27232291
(4885136)
 OTHER
Adrenal extramedullary hematopoiesis associated with beta-thalassemia trait in an adult woman: a case report and review of literature.
Al-Thani H, Al-Sulaiti M, El-Mabrok G, Tabeb A, El-Menyar A.
Int J Surg Case Rep. 2016;24:83-7.
Adrenal extramedullary hematopoiesis associated with beta-thalassemia trait in an adult woman: a case report and review of literature.
24717020
 MIXED_SAMPLE Adult
Hydroxyurea as a first-line treatment of extramedullary hematopoiesis in patients with beta thalassemia: Four case reports.
Karimi M, Cohan N, Pishdad P.
Hematology. 2015;20(1):53-7.
Hydroxyurea as a first-line treatment of extramedullary hematopoiesis in patients with beta thalassemia: Four case reports.
22438693
(3303909)
 MALE
Intracranial extramedullary hematopoiesis in beta-thalassemia.
Karki B, Xu YK, Tamrakar K, Wu YK.
Korean J Radiol. 2012;13(2):240-3.
Intracranial extramedullary hematopoiesis in beta-thalassemia.
22182855
(3285055)
 OTHER
An intracranial extramedullary hematopoiesis in a 34-year-old man with beta thalassemia: a case report.
Tabesh H, Shekarchizadeh A, Mahzouni P, Mokhtari M, Abrishamkar S, Abbasi Fard S.
J Med Case Rep. 2011;5:580.
An intracranial extramedullary hematopoiesis in a 34-year-old man with beta thalassemia: a case report.
19488015
 FEMALE Middle Aged
Cardiac myxoma showing extramedullary hematopoiesis in a patient with beta thalassemia.
Joukhadar R, De Las Casas LE, Lalude O, Gough D.
South Med J. 2009;102(7):769-71.
Cardiac myxoma showing extramedullary hematopoiesis in a patient with beta thalassemia.
18552471
 MALE
Management of spinal cord compression caused by extramedullary hematopoiesis in beta-thalassemia.
Moncef B, Hafedh J.
Intern Med. 2008;47(12):1125-8.
Management of spinal cord compression caused by extramedullary hematopoiesis in beta-thalassemia.
16533417
 MALE Adult
Massive hemothorax in a beta-thalassemic patient due to spontaneous rupture of extramedullary hematopoietic masses: diagnosis and successful treatment.
Pornsuriyasak P, Suwatanapongched T, Wangsuppasawad N, Ngodngamthaweesuk M, Angchaisuksiri P.
Respir Care. 2006;51(3):272-6.
We report a case of a 38-year-old man with underlying beta thalassemia/hemoglobin E who developed intrathoracic extramedullary hematopoiesis.
15771316
 MALE Adult
[Cord compression secondary to extramedullary hematopoiesis in a patient with beta-thalassaemia].
Mutijima E, Hmissa S, Ziadi S, Mlaiki A, Mokni M, Korbi S.
Rev Med Liege. 2005;60(1):41-4.
Extramedullary hematopoiesis (EMH) is a common manifestation in beta-thalassemia, but can also occur in several clinical hematologic disorders or neoplasms.
15075694
 MALE Adult
Fatal hemothorax due to rupture of an intrathoracic extramedullary hematopoietic nodule.
Chute DJ, Fowler DR.
Am J Forensic Med Pathol. 2004;25(1):74-7.
We report a case of a 26-year-old African-American male with a past medical history of sickle cell trait/beta thalassemia who developed multiple intrathoracic nodules of extramedullary hematopoiesis.
15545849
 MALE Adult
Intrathoracic masses due to extramedullary hematopoiesis.
Castelli R, Graziadei G, Karimi M, Cappellini MD.
Am J Med Sci. 2004;328(5):299-303.
We describe massive intrathoracic extramedullary hematopoiesis in a 41-year-old man with compound heterozygosis for beta-thalassemia and sickle cell anemia and functional asplenia.
12452605
 FEMALE Child
Adrenal extramedullary hematopoiesis: report on a pediatric case and update of the literature.
Porcaro AB, Novella G, Antoniolli SZ, Martignoni G, Brunelli M, Curti P.
Int Urol Nephrol. 2001;33(4):601-3.
The authors report on a rare pediatric case of adrenal extramedullary hematopoiesis in a patient with beta-thalassemia disease.
10844371
 MALE Adult
[Spinal cord compression secondary to extramedullary hematopoiesis in a patient with thalassemia].
Bruneteau G, Fenelon G, Khalil A, Kanfer A, Girot R.
Rev Neurol (Paris). 2000;156(5):510-3.
A 19-year-old man with homozygous beta thalassemia presented with signs of thoracic spinal cord compression secondary to extramedullary hematopoiesis.
9650475
 FEMALE Adult
Adrenal extramedullary hematopoietic tumor in a patient with beta-thalassemia.
Chuang CK, Chu SH, Fang JT, Wu JH.
J Formos Med Assoc. 1998;97(6):431-3.
We report a case of adrenal extramedullary hematopoiesis in a 27-year-old woman with beta-thalassemia.
9673716
 MALE Middle Aged
Scintigraphic diagnosis of intrathoracic extramedullary hematopoiesis in a patient with beta-thalassemia.
Ozdemir A, Gungor F, Tuncdemir F, Cubuk M, Karayalcin B.
Ann Nucl Med. 1998;12(3):149-51.
We report the scintigraphic diagnosis of intrathoracic extramedullary hematopoiesis (EMH) in a patient with beta-thalassemia.
9673716
 MALE Middle Aged
Scintigraphic diagnosis of intrathoracic extramedullary hematopoiesis in a patient with beta-thalassemia.
Ozdemir A, Gungor F, Tuncdemir F, Cubuk M, Karayalcin B.
Ann Nucl Med. 1998;12(3):149-51.
Scintigraphic diagnosis of intrathoracic extramedullary hematopoiesis in a patient with beta-thalassemia.
9574659
 MALE Adult
Visual failure caused by suprasellar extramedullary hematopoiesis in beta thalassemia: case report.
Aarabi B, Haghshenas M, Rakeii V.
Neurosurgery. 1998;42(4):922-5; discussion 925-6.
Visual failure caused by suprasellar extramedullary hematopoiesis in beta thalassemia: case report.
9111677
 MALE
MR of thoracic cord compression caused by epidural extramedullary hematopoiesis in myelodysplastic syndrome.
Dibbern DA Jr, Loevner LA, Lieberman AP, Salhany KE, Freese A, Marcotte PJ.
AJNR Am J Neuroradiol. 1997;18(2):363-6.
Spinal cord compression caused by extramedullary hematopoiesis is a rare complication of chronic anemic states, most frequently occurring in patients with beta-thalassemia.
7554666
 MALE Middle Aged
Fe-52 imaging of intrathoracic extramedullary hematopoiesis in a patient with beta-thalassemia.
Adams BK, Jacobs P, Byrne MJ, Bird AR, Boniaczszuk J.
Clin Nucl Med. 1995;20(7):619-22.
Fe-52 imaging of intrathoracic extramedullary hematopoiesis in a patient with beta-thalassemia.