Beta-thalassemia

Beta-thalassemia (BT) is characterized by deficiency (Beta+) or absence (Beta0) of synthesis of the beta globin chains of hemoglobin (Hb).

Hypercoagulability

An abnormality of coagulation associated with an increased risk of thrombosis.


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PMID (PMCID)
16427892
 FEMALE Middle Aged
Aortic valve replacement in a patient with thalassemia intermedia.
Farmakis D, Polonifi A, Deftereos S, Tsironi M, Papaioannou I, Aessopos A.
Ann Thorac Surg. 2006;81(2):737-9.
Pseudoxanthoma elasticum-like diffuse elastic tissue defects and hypercoagulability are two well-established features in beta-thalassemia, which play a key role in the development of a spectrum of collateral complications in these patients.