AL amyloidosis

A plasma cell disorder characterized by the aggregation and deposition of insoluble amyloid fibrils derived from misfolding of monoclonal immunoglobulin light chains usually produced by a plasma cell tumor. It usually presents as primary systemic amyloidosis (PSA) with multiple organ involvement and less frequently as primary localized amyloidosis (PLA) restricted to a single organ.

Ascites

Accumulation of fluid in the peritoneal cavity.


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PMID (PMCID)
20695302
 OTHER
[Amyloidosis--uncommon etiology for ascites].
Laitinen T, Kiviniemi M, Heikkinen M.
Duodecim. 2010;126(13):1591-4.
We present a patient who had primary (AL) amyloidosis as the reason for remarkable amount of ascites.
1858771
 FEMALE Adult
Computed tomography for diagnosis of hepatic rupture in primary systemic amyloidosis.
Gastineau DA, Gertz MA, Rosen CB, Kyle RA.
Am J Hematol. 1991;37(3):194-6.
In the setting of primary amyloidosis, the early use of CT scanning for undiagnosed ascites, hypotension, or rapid organ enlargement may lead to early diagnosis and potential surgical correction.