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AL amyloidosis

A plasma cell disorder characterized by the aggregation and deposition of insoluble amyloid fibrils derived from misfolding of monoclonal immunoglobulin light chains usually produced by a plasma cell tumor. It usually presents as primary systemic amyloidosis (PSA) with multiple organ involvement and less frequently as primary localized amyloidosis (PLA) restricted to a single organ.

Ventricular arrhythmia

Total: 1

(per page)

PMID (PMCID)
25535224	FEMALE	Middle Aged
	Life-saving implantable cardioverter defibrillator therapy in cardiac AL amyloidosis.
	Patel KS, Hawkins PN, Whelan CJ, Gillmore JD. BMJ Case Rep. 2014;2014:.
	We describe a patient who presented with cardiac AL amyloidosis who underwent prophylactic ICD implantation for the prevention of sudden cardiac death during treatment with chemotherapy, in whom life-threatening ventricular arrhythmia was successfully terminated over a 3-year period.