AL amyloidosis

A plasma cell disorder characterized by the aggregation and deposition of insoluble amyloid fibrils derived from misfolding of monoclonal immunoglobulin light chains usually produced by a plasma cell tumor. It usually presents as primary systemic amyloidosis (PSA) with multiple organ involvement and less frequently as primary localized amyloidosis (PLA) restricted to a single organ.

Chylothorax

Accumulation of excessive amounts of lymphatic fluid (chyle) in the pleural cavity.

Total: 2

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PMID (PMCID)
18535528	MALE
	[An unusual cause of chylothorax: primary amyloidosis].
	Jeannin G, Marson H, Merle P, Janicot H, Greil A, Caillaud D. Rev Mal Respir. 2008;25(5):601-4.
	[An unusual cause of chylothorax: primary amyloidosis].
18535528	MALE
	[An unusual cause of chylothorax: primary amyloidosis].
	Jeannin G, Marson H, Merle P, Janicot H, Greil A, Caillaud D. Rev Mal Respir. 2008;25(5):601-4.
	We report an original case of primary amyloidosis presenting as a chylothorax and confirmed by an endomyocardial biopsy.