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AL amyloidosis

A plasma cell disorder characterized by the aggregation and deposition of insoluble amyloid fibrils derived from misfolding of monoclonal immunoglobulin light chains usually produced by a plasma cell tumor. It usually presents as primary systemic amyloidosis (PSA) with multiple organ involvement and less frequently as primary localized amyloidosis (PLA) restricted to a single organ.

Hypoxemia

An abnormally low level of blood oxygen.

Total: 1

(per page)

PMID (PMCID)
27357815	MALE	Middle Aged
	Bortezomib therapy-related lung disease in a patient with light chain amyloidosis: A case report.
	Balsman E. J Oncol Pharm Pract. 2017;23(7):545-548.
	This report describes a 57-year-old patient with light chain (primary) amyloidosis receiving weekly subcutaneous bortezomib injections who presented with recurrent hypoxemia and interstitial pneumonitis.