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AL amyloidosis

A plasma cell disorder characterized by the aggregation and deposition of insoluble amyloid fibrils derived from misfolding of monoclonal immunoglobulin light chains usually produced by a plasma cell tumor. It usually presents as primary systemic amyloidosis (PSA) with multiple organ involvement and less frequently as primary localized amyloidosis (PLA) restricted to a single organ.

Oligoarthritis

Total: 1

(per page)

PMID (PMCID)
24633430	MALE	Middle Aged
	[A 48-year-old patient with oligoarthritis of the knees, having excluded spondyloarthritis and rheumathoid arthritis].
	Gehlen M, Janik S, Dudko P, Schwarz-Eywill M. Internist (Berl). 2014;55(4):443-7.
	We report the case of a patient with amyloid light-chain (AL) amyloidosis, presenting for more than 1.5years with oligoarthritis as the only clinical symptom of the underlying disease.