Wilson disease

Wilson disease is a very rare inherited multisystemic disease presenting non-specific neurological, hepatic, psychiatric or osseo-muscular manifestations due to excessive copper deposition in the body.

Macronodular cirrhosis

A type of cirrhosis characterized by the presence of large regenerative nodules.


Total: 1

                      


(per page)
PMID (PMCID)
11407524
MALE Adult
Electron microscopic detection of copper in the liver of two patients with morbus Wilson by EELS and EDX.
Jonas L, Fulda G, Salameh T, Schmidt W, Kroning G, Hopt UT, Nizze H.
Ultrastruct Pathol. 2001;25(2):111-8.
The explanted liver showed a strong macronodular cirrhosis as typically seen in Wilson disease.